Springer Science and Business Media LLC

We report here a classic case of dysembryoplastic neuroepithelial tumour, which was situated in the left frontal lobe of a 13-year-old boy who presented with intractable partial complex seizures since 3 years of age. This tumour entity was first described in 1988, and has been incorporated in the 2nd edition (1993) of the WHO histological typing of CNS tumours. Fewer than 100 cases have been reported from all over the world. To our knowledge, this is the first report of this tumour from India. It is important to recognise this entity since surgery is the only means of cure and radio- or chemotherapy is unwarranted.