Pharmacological chaperones facilitate the post-ER transport of recombinant N370S mutant β-glucocerebrosidase in plant cells: Evidence that N370S is a folding mutant

Molecular Genetics and Metabolism - Tập 106 - Trang 323-329 - 2012
Gholamreza Babajani1, Michael B. Tropak2, Don J. Mahuran2,3, Allison R. Kermode1
1Department of Biological Sciences, Simon Fraser University, 8888 University Dr., Burnaby, BC, Canada V5A 1S6
2Research Institute, Hospital for Sick Children, 555 University Avenue, Toronto, Ontario, Canada M5G 1X8
3Department of Laboratory Medicine and Pathology, University of Toronto, Banting Institute, 100 College Street, Toronto, Ontario, Canada M5G 1L5

Tài liệu tham khảo

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