Mechanisms of fingolimod's efficacy and adverse effects in multiple sclerosis

Annals of Neurology - Tập 69 Số 5 - Trang 759-777 - 2011
Jeffrey A. Cohen1, Jerold Chun2
1Mellen Center for Multiple Sclerosis Treatment and Research, Neurological Institute, Cleveland Clinic, Cleveland, OH
2Department of Molecular Biology, Dorris Neuroscience Center, Scripps Research Institute, La Jolla, CA

Tóm tắt

Abstract

Until recently, all approved multiple sclerosis (MS) disease treatments were administered parenterally. Oral fingolimod was approved in September 2010 by the US Food and Drug Administration to reduce relapses and disability progression in relapsing forms of MS. In the clinical trials that led to approval, fingolimod reduced not only acute relapses and magnetic resonance imaging lesion activity but also disability progression and brain volume loss, suggesting preservation of tissue. Fingolimod's mechanism of action in MS is not known with certainty. Its active form, fingolimod‐phosphate (fingolimod‐P), is a sphingosine 1‐phosphate receptor (S1PR) modulator that inhibits egress of lymphocytes from lymph nodes and their recirculation, potentially reducing trafficking of pathogenic cells into the central nervous system (CNS). Fingolimod also readily penetrates the CNS, and fingolimod‐P formed in situ may have direct effects on neural cells. Fingolimod potently inhibits the MS animal model, experimental autoimmune encephalomyelitis, but is ineffective in mice with selective deficiency of the S1P1 S1PR subtype on astrocytes despite normal expression in the immune compartment. These findings suggest that S1PR modulation by fingolimod in both the immune system and CNS, producing a combination of beneficial anti‐inflammatory and possibly neuroprotective/reparative effects, may contribute to its efficacy in MS. In clinical trials, fingolimod was generally safe and well tolerated. Its interaction with S1PRs in a variety of tissues largely accounts for the reported adverse effects, which were seen more frequently with doses 2.5 to 10× the approved 0.5mg dose. Fingolimod's unique mechanism of action distinguishes it from all other currently approved MS therapies. Ann Neurol 2011;69:759–777

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Tài liệu tham khảo

10.1056/NEJMra052130

10.1056/NEJMoa010994

10.1093/brain/awl217

10.1007/s00415-008-6014-x

10.1007/BF00184787

10.1146/annurev.immunol.22.012703.104702

10.1056/NEJMp068159

10.1038/nrm1103

10.1002/jcb.20097

10.1006/abio.1999.4157

10.1146/annurev.pharmtox.41.1.507

10.1016/S1043-6618(03)00046-X

10.1146/annurev.biochem.73.011303.073731

10.1124/pr.110.003111

10.1096/fj.02-0548com

10.1096/fj.03-0910fje

10.1084/jem.20041509

10.1126/science.1113640

10.1016/S0165-6147(02)00012-3

10.1111/j.1365-2125.2003.02065.x

10.1002/bdd.535

10.1034/j.1600-6143.2003.00130.x

10.1097/01.TP.0000084822.01372.AC

10.1177/0091270004264165

10.1177/0091270005279799

10.1124/dmd.105.009001

10.1124/jpet.107.127183

10.1074/jbc.C200176200

10.1126/science.1070238

10.1074/jbc.M307687200

10.1016/S0014-5793(03)01168-2

10.1074/jbc.M406512200

10.1074/jbc.M506293200

10.1182/blood-2005-07-2628

10.1074/jbc.M610318200

10.1038/nchembio.173

10.1038/nature02284

10.1074/jbc.M311743200

10.1056/NEJMoa052643

10.1056/NEJMoa0909494

10.1056/NEJMoa0907839

Montalban X, 2009, Oral fingolimod (FTY720) shows sustained low rates of clinical and MRI disease activity in patients with relapsing multiple sclerosis: four‐year results from a phase II extension (P06.128) [abstract], Neurology, 72, A313

10.1212/WNL.53.8.1698

10.1212/01.WNL.0000149516.30155.B8

10.1212/01.wnl.0000260064.77700.fd

10.1097/01.TP.0000121761.02129.A6

10.1111/j.1600-6143.2006.01552.x

10.1097/01.tp.0000251718.95622.b3

10.1590/S0100-879X2005000500005

Francis G, 2010, Lymphocytes and fingolimod—temporal pattern and relationship with infections (P442), Mult Scler, 16, S146

10.1016/j.clim.2010.06.005

10.1093/ndt/gfg599

10.1046/j.1365-2567.1998.00639.x

10.1016/j.intimp.2006.07.030

10.1212/WNL.0b013e3181ebdd64

10.1038/nm.2110

10.1212/01.wnl.0000327609.57688.ea

10.1111/j.1476-5381.2009.00451.x

10.1084/jem.20061289

10.4049/jimmunol.160.10.5037

10.1016/S0041-1345(00)02126-6

10.4049/jimmunol.170.7.3662

10.1128/MCB.25.24.11113-11121.2005

10.1093/hmg/ddn126

10.1634/stemcells.2006-0223

10.1111/j.1471-4159.2004.02955.x

10.1016/S0014-5793(97)01277-5

10.1046/j.1471-4159.2000.0750503.x

10.1002/glia.20324

10.1073/pnas.1014154108

10.1002/glia.20546

10.1007/s00018-008-8059-5

10.1046/j.0953-816x.2001.01585.x

10.1042/BJ20020867

10.1124/mol.64.5.1199

10.1016/S0006-8993(03)03527-3

10.1016/j.ijdevneu.2004.03.005

10.1111/j.1471-4159.2007.04629.x

van Doorn R, 2010, Sphingosine 1‐phosphate receptors 1 and 3 are upregulated in multiple sclerosis lesions (P662), Mult Scler, 16, S228

10.1016/S0169-328X(99)00279-X

10.1074/jbc.M011570200

10.1006/mcne.1999.0776

10.1074/jbc.275.19.14281

10.1016/j.pharmthera.2007.08.005

10.1016/S0306-4522(02)00791-1

10.1523/JNEUROSCI.4645-04.2005

10.1002/glia.10297

10.1002/glia.20576

10.1096/fj.06-7420com

10.2353/ajpath.2008.080478

10.1002/ana.21227

10.1016/j.jns.2008.06.031

10.1124/jpet.107.123927

10.1016/S1043-6618(03)00049-5

10.1046/j.1471-4159.2003.02219.x

10.1016/S0014-5793(02)03404-X

10.1002/j.1460-2075.1996.tb00595.x

10.1006/bbrc.1997.7666

10.1074/jbc.274.8.4626

10.1523/JNEUROSCI.17-18-06952.1997

10.1016/S0306-4522(02)00539-0

10.1128/MCB.01465-06

Deogracias R, 2008, Expression of brain‐derived neurotrophic factor is regulated by fingolimod (FTY720) in cultured neurons (P728), Mult Scler, 14, S243

Kataoka H, 2005, FTY720, sphingosine 1‐phosphate receptor modulator, ameliorates experimental autoimmune encephalomyelitis by inhibition of T cell infiltration, Cell Mol Immunol, 2, 439

10.1016/j.brainresbull.2007.06.023

Pryce G, 2008, Control of chronic relapsing progressive EAE with fingolimod (P01.092), Neurology, 70, A29

10.1002/jnr.22196

10.1016/j.jneuroim.2004.04.015

Schubart AS, 2008, FTY720 suppresses ongoing EAE and promotes a remyelinating environment preventing axonal degeneration within the CNS (P06.166), Neurology, 70, A339

Rossi S, 2010, Fingolimod treatment prevents the clinical, synaptic and dendritic abnormalities of experimental autoimmune encephalomyelitis (P880), Mult Scler, 16, S309

Schubart A, 2007, CNS mediated effects of FTY720 (fingolimod) (P07.101), Neurology, 68, A315

Anthony DC, 2010, Fingolimod (FTY720) therapy reduces demyelination and microglial activation in a focal delayed‐type hypersensitivity model of multiple sclerosis during the remission phase (P814), Mult Scler, 16, S283

10.1111/j.1582-4934.2007.00019.x

10.1620/tjem.219.295

Collins W, 2010, Long‐term safety of oral fingolimod (FTY720) in relapsing multiple sclerosis: integrated analyses of phase 1 and 3 studies (P843), Mult Scler, 16, S295

NDA 02257—FDA approved labeling text for Gilenya (fingolimod) capsules. September 21 2010. Available at:http://www.accessdata.fda.gov/drugsatfda_docs/label/2010/022527s000lbl.pdf. Accessed March 23 2011.

10.1016/j.coph.2006.09.008

10.1177/002215540205000507

10.1042/bj3550189

10.1111/j.1600-6143.2005.00754.x

10.1124/jpet.103.062828

Gergely P, 2009, Phase I study with the selective S1P1/S1P5 receptor modulator BAF312 indicates that S1P1 rather than S1P3 mediates transient heart rate reduction in humans (P437), Mult Scler, 15, S125

10.1177/0091270006289853

DiMarco JP, 2010, First‐dose effect of fingolimod: pooled safety data from two phase 3 studies (TRANSFORMS and FREEDOMS) (P830), Mult Scler, 16, S290

10.1172/JCI10905

10.1016/j.prostaglandins.2004.01.006

10.4049/jimmunol.175.11.7151

10.1111/j.1600-6143.2004.00476.x

10.1002/jcb.20088

10.1016/j.coph.2005.12.004

10.1038/nrd2356

10.1016/S0014-2999(03)01731-X

10.1038/nri1650

10.1161/01.RES.0000164321.91452.00

10.1056/NEJMoa0907839

10.1186/1465-9921-6-48

10.1124/jpet.106.110718

10.1165/rcmb.2006-0383OC

10.4049/jimmunol.164.11.5761

Schmouder R, 2010, Effects of fingolimod on antibody response following steady‐state dosing in healthy volunteers: a 4‐week randomised, placebo‐controlled study (P412), Mult Scler, 16, S135

Novartis. FTY720 in patients with primary progressive multiple sclerosis (INFORMS). ClinicalTrials.gov Identifier: NCT00731692. Available at:http://clinicaltrials.gov/ct2/show/NCT00731692. Accessed March 23 2011.

Khatri B, 2010, 24‐month efficacy and safety from the TRANSFORMS extension study of oral fingolimod (FTY720) in patients with relapsing‐remitting multiple sclerosis(P03.125), Neurology, 74, A239

Calabresi PA, 2010, Oral fingolimod (FTY720) in relapsing‐remitting multiple sclerosis: baseline patient demographics and disease characteristics from a 2‐year phase III trial (FREEDOMS II) (P05.038), Neurology, 74, A416

Novartis. Efficacy and safety of fingolimod (FTY720) in patients with relapsing‐remitting multiple sclerosis (FREEDOMS II). ClinicalTrials.gov Identifier: NCT00355134. Available at:http://clinicaltrials.gov/ct2/show/NCT00355134. Accessed March 23 2011.

Novartis and Mitsubishi Tanabe Pharma. Efficacy and safety of FTY720 in patients with relapsing multiple sclerosis (MS). ClinicalTrials.gov Identifier: NCT00537082. Available at:http://clinicaltrials.gov/ct2/show/NCT00537082. Accessed March 23 2011.

10.1371/journal.pone.0004112

10.1016/j.bbrc.2007.02.043

10.1111/j.1471-4159.2005.03451.x