Enzyme replacement therapy with alglucosidase alfa in 44 patients with late-onset glycogen storage disease type 2: 12-month results of an observational clinical trial

S. Strothotte1, N. Strigl-Pill1, Birgit Grunert2, Cornelia Kornblum3, K. Eger4, Carsten Wessig5, Marcus Deschauer4, Frank Breunig6, Franz Xaver Glocker7, Stefan Vielhaber8, Andrea Brejova8, M. J. Hilz9, Karlheinz Reiners5, Wolfgang Müller‐Felber10, Eugen Mengel11, Matthias Spranger2, Benedikt Schöser1
1Department of Neurology, Friedrich Baur Institute, Ludwig Maximilian University Munich, Ziemssenstr. 1a, 80336, Munich, Germany
2Neurologisches Rehabilitationszentrum Friedehorst, Bremen, Germany
3Department of Neurology, University Hospital of Bonn, Bonn, Germany
4Department of Neurology, Martin Luther University Halle-Wittenberg, Halle, Germany
5Department of Neurology, Julius Maximilian University Würzburg, Würzburg, Germany
6Department of Nephrology, Julius Maximilian University Würzburg, Würzburg, Germany
7Department of Neurology, University Hospital Freiburg, Freiburg, Germany
8Department of Neurology, University Hospital Magdeburg, Magdeburg, Germany
9Department of Neurology, University Erlangen, Erlangen, Germany
10Department of Neuropediatrics, Ludwig Maximilian University Munich, Munich, Germany
11Department of Paediatrics, Johannes Gutenberg University Mainz, Mainz, Germany

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