Diagnosis and treatment of hereditary angioedema with normal C1 inhibitor

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Bork K, Hardt J, Schicketanz KH, Ressel N: Clinical studies of sudden upper airway obstruction in patients with hereditary angioedema due to c1 esterase inhibitor deficiency. Arch Intern Med. 2003, 163: 1229-1235. 10.1001/archinte.163.10.1229.

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Bork K: Hereditary angioedema with normal C1 inhibitor activity including hereditary angioedema with coagulation factor XII gene mutations. Immunol Allergy Clin North Am. 2006, 26: 709-724. 10.1016/j.iac.2006.09.003.