Cystic fibrosis: An update for clinicians. Part 1: Nutrition and gastrointestinal complications

Journal of Gastroenterology and Hepatology (Australia) - Tập 29 Số 7 - Trang 1344-1355 - 2014
Wolfram Haller1, Oren Ledder1, Peter Lewindon2, Richard Couper3, Kevin Gaskin4, Mark Oliver1
1Department of Gastroenterology and Clinical Nutrition, Royal Children’s Hospital, Parkville, Victoria, Australia
2Department of Gastroenterology, Royal Children's Hospital, Brisbane, Queensland, Australia
3Department of Gastroenterology, Women's and Children's Hospital, North Adelaide, South Australia, Australia
4Department of Gastroenterology, The Children's Hospital at Westmead, Sydney, New South Wales, Australia

Tóm tắt

AbstractDuring three decades, the demographics of cystic fibrosis (CF) has undergone a significant change. Advances in nutritional and pulmonary management allow the vast majority of patients reaching adulthood today. With increasing survival, new and previously less common aspects of CF are encountered by the clinician expanding the concept of CF as a multisystem disease. The first part of this two‐part review will focus on the nutritional and gastrointestinal aspects of the CF phenotype and outline core principles of diagnosis and care.

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