Correction of aortic coarctation in a girl with severe PHACE syndrome

Journal of Cardiothoracic Surgery - Tập 9 - Trang 1-4 - 2014
Lian Xiong1, Zhenkun Xia1, Chengming Fan1, Weizhi Zhang1, Jinfu Yang1
1Department of the cardiothoracic surgery, The 2nd Xiangya Hospital, Central South University, Changsha, China

Tóm tắt

A 12-year-old Chinese girl was demonstrated multivessel distortion and malformation: aortic coarctation with the narrowest lumen diameter measuring of 4 mm located between the left common carotid artery and the left subclavian artery, a huge and thin-walled aneurysm is connected to the coarctation, and the descending aorta was distorted. Cerebrovascular revealed distorted arteries and a completely aberrant brain blood supply. She underwent correction of the aortic coarctation by establishing a bypass between the ascending aorta and the descending aorta using a 13-mm Gore-tex tube. Postoperative recovery was uneventful, at 6-month follow-up, the cervical vascular pulsatility was relieved and she is in good condition.

Tài liệu tham khảo

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