Biochemical and molecular diagnosis of lipoamide dehydrogenase deficiency in a North American Ashkenazi Jewish family

Journal of Inherited Metabolic Disease - Tập 29 - Trang 203-204 - 2006
C. Sansaricq1, S. Pardo1, M. Balwani1, M. Grace1, K. Raymond1
1Department of Human Genetics, Mount Sinai School of Medicine, New York, USA

Tóm tắt

A late-onset presentation of lipoamide dehydrogenase (E3) deficiency is described in a North American Ashkenazi Jewish (AJ) family. Diagnosis was made by urine organic acid and molecular analyses.

Tài liệu tham khảo

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