Aging-Dependent Large Accumulation of Point Mutations in the Human mtDNA Control Region for Replication

American Association for the Advancement of Science (AAAS) - Tập 286 Số 5440 - Trang 774-779 - 1999
Yuichi Michikawa1, Franca Mazzucchelli2, Nereo Bresolin2, G. Scarlato2, Giuseppe Attardi1
1Division of Biology, California Institute of Technology, Pasadena, CA 91125 USA
2University of Milan, Institute of Clinical Neurology, Dino Ferrari Center, IRCCS, and Ospedale Maggiore di Milano–Policlinico, IRCCS E. Medea–Bosisio Parini (LC), 20122 Milan, Italy.

Tóm tắt

Progressive damage to mitochondrial DNA (mtDNA) during life is thought to contribute to aging processes. However, this idea has been difficult to reconcile with the small fraction of mtDNA so far found to be altered. Here, examination of mtDNA revealed high copy point mutations at specific positions in the control region for replication of human fibroblast mtDNA from normal old, but not young, individuals. Furthermore, in longitudinal studies, one or more mutations appeared in an individual only at an advanced age. Some mutations appeared in more than one individual. Most strikingly, a T414G transversion was found, in a generally high proportion (up to 50 percent) of mtDNA molecules, in 8 of 14 individuals above 65 years of age (57 percent) but was absent in 13 younger individuals.

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See (38) for methods for fibroblast culture and first DGGE analysis.

Methods for mtDNA cloning and second-DGGE analysis can be found in (38) .

The method for sequencing is described in (38).

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A repeat of the cloning and sequencing of the DLP6 fragments of the two LS6 samples gave results that when combined with the previous ones yielded a coefficient of variation for the frequency of the specific point mutations of ∼20% supporting the reproducibility of the estimates. Therefore it is possible that the observed decrease in the T414G mutation frequency in the LS6-82 y sample results from a difference in the biopsy site or from handling of the original specimen.

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Supplemental material is available at the Science Web site (www.sciencemag.org/feature/data/1040395.shl).

Supported by National Institute on Aging (NIH) grant AG12117-03 (to G.A.). We thank A. Chomyn and G. Villani for valuable discussions M. Lai for support A. Aman R. Steinberger and M. Scott for their help with experiments and A. Drew B. Keeley R. Zedan and C. Lin for expert technical assistance.