A case of Arrhythmogenic right ventricular cardiomyopathy without arrhythmias

Diagnostic Pathology - 2012
Jia Wei1, Jiang Tang1, Liming Xia2, Xinshan Chen3, Dao Wen Wang1
1Department of Internal Medicine, Tongji Hospital; Tongji Medical College, Huazhong University of Science and Technology, Wuhan, China
2Department of Radiology, Tongji Hospital, Tongji Medical College, Huazhong University of Science and Technology, Wuhan, China
3Department of Forensic Pathology, Tongji Medical College, Huazhong University of Science and Technology, Wuhan, China

Tóm tắt

Abstract Arrhythmogenic right ventricular cardiomyopathy (ARVC) is characterized by recurrent coma, ventricular tachycardias and the replacement of the myocardium with fatty and fibrous tissue. We described a 42-year-old female patient without clinical arrhythmias which was diagnosed as ARVC by magnetic resonance imaging (MRI), but the transvenous endomyocardial biopsy was not specific. The patient received heart transplantation due to her refractory heart failure and the pathology of explanted heart demonstrated typical replacement of fatty and fibrous tissue and piles of infiltrated lymphocytes in myocardial tissue. It is concluded that ARVC might not have any arrhythmias and inflammatory process may be involved in the mechanism of ARVC. Virtual slides The virtual slide(s) for this article can be found here:http://www.diagnosticpathology.diagnomx.eu/vs/6573514507145351

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