A Rapid Fluorogenic Palmitoyl-Protein Thioesterase Assay: Pre- and Postnatal Diagnosis of INCL

Molecular Genetics and Metabolism - Tập 66 Số 4 - Trang 240-244 - 1999
O. P. van Diggelen1, J. L. M. Keulemans1, Bryan Winchester2, I. L. Hofman3, Sanna‐Leena Vanhanen4, Pirkko Santavuori4, Ya. V. Voznyi5
1Department of Clinical Genetics, Erasmus University, 3000 DR, Rotterdam, The Netherlands
2Institute of Child Health, London, United Kingdom
3Bartimeushage, Doorn, The Netherlands
4Department of Paediatric Neurology, Hospital for Children and Adolescents, Helsinki, Finland
5Institute of Organic Chemistry, Moscow, Russia

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