Locomotor deficits in the mutant mouse, Lurcher

Springer Science and Business Media LLC - Tập 66 - Trang 271-286 - 1987
P. A. Fortier1, A. M. Smith1, S. Rossignol1
1Centre de Recherche en Sciences Neurologiques, Département de Physiologie, Université de Montréal, Montréal, Canada

Tóm tắt

The effect of total Purkinje cell degeneration on treadmill locomotion was studied in the cerebellar mutant mouse Lurcher. Other movements such as swimming and scratchting were also studied in order to evaluate the cerebellar control of rhythmic actions. Cinematographic and electromyographic recordings were taken from normal and Lurcher mice that were subsequently perfused to obtain a Purkinje cell count. Walking deteriorated progressively and was clearly abnormal in 30 day old Lurchers with 90% Purkinje cell degeneration. In adult Lurcher mice in which Purkinje cells were totally absent, walking was characterized by short steps with exaggerated hindlimb flexion in the swing phase. Also, both the interlimb step ratio, defined as the step length of the reference limb divided by the step length of the opposite limb, and the interlimb coupling, defined as the temporal relation of one footfall with respect to the footfall of another limb, varied more than in normal mice. Furthermore, the locomotion of Lurcher mice displayed increased vertical displacement of the hip and an inability to produce continuous step cycles without stumbling. Both the EMG onset relative to foot contact and the EMG burst duration were highly variable, and a greater overlap in the activities of antagonist muscles at the transition from ankle extension to flexion was evident. Although both walking and swimming involve cyclical limb movements, the disorganization of the cycle and the irregular EMG pattern seen in the Lurcher during walking were not observed during swimming. Furthermore, scratching was well executed in the Lurcher mice. However, a consistently higher tonic extensor activity at the ankle appeared during walking, swimming and scratching. These results suggest that, in contrast to swimming and scratching, the requirements of walking depend to a greater degree on a functional cerebellar cortex for successful performance.

Tài liệu tham khảo

Antziferora LI, Arshavsky YI, Orlovsky GN, Pavlova GA (1980) Activity of neurons of cerebellar nuclei during fictitious scratch reflex in the cat. I. Fastigial nucleus. Brain Res 200: 239–248 Armstrong DM, Edgley SA (1984a) Discharges of nucleus interpositus neurones during locomotion in the cat. J Physiol 351: 411–432 Armstrong DM, Edgley SA (1984b) Discharges of Purkinje cells in the paravermal part of the cerebellar anterior lobe during locomotion in the cat. J Physiol 352: 403–424 Arshavsky YI, Gelfand IM, Orlovsky GN, Pavlova GA (1978a) Messages conveyed by spinocerebellar pathways during scratching in the cat. I. Activity of neurons of the lateral reticular nucleus. Brain Res 151: 479–491 Arshavsky YI, Gelfand IM, Orlovsky GN, Pavlova GA (1978b) Messages conveyed by spinocerebellar pathways during scratching in the cat. II. Activity of neurons of the ventral spinocerebellar tract. Brain Res 151: 493–506 Arshavsky YI, Gelfand IM, Orlovsky GN, Pavlova GA (1978c) Messages conveyed by descending tracts during scratching in the cat. I. Activity of vestibulospinal neurons. Brain Res 159: 99–110 Arshavsky YI, Orlovsky GN, Pavlova GA, Perret C (1978d) Messages conveyed by descending tracts during scratching in the cat. II. Activity of rubrospinal neurons. Brain Res 159: 111–123 Arshavsky YI, Orlovsky GN, Pavlova GA, Perret C (1980) Activity of neurons of cerebellar nuclei during fictitious scratch reflex in the cat. II. Interpositus and lateral nuclei. Brain Res 200: 249–258 Babinski J (1902) Sur le rôle du cervelet dans les actes volitionnels nécessitant une succession rapide des mouvements (Diadococinésie). Rev Neurol 10: 1013–1014 Caddy KWT, Biscoe TJ (1979) Structural and quantitative studies of the normal C3H and Lurcher mutant mouse. Philos Trans R Soc Lond 287: 167–201 Caddy KWT, Martin MR, Biscoe TJ (1977) The identification of mossy fibers and their cells or origin in the normal and Lurcher mutant mouse. J Neurol Sci 34: 121–129 Chambers WW, Sprague JM (1955) Functional localization in the cerebellum. II. Somatotopic organization in cortex and nuclei. Arch Neurol Psychiat 74: 653–680 Dixon WJ, Massey FJ Jr (1969) Introduction to statistical methods, 3rd edn. McGraw-Hill, Toronto Dow RS, Moruzzi G (1958) The physiology and pathology of the cerebellum. The University of Minnesota Press, Minneapolis Frysinger RC, Bourbonnais D, Kalaska JF, Smith AM (1984) Cerebellar cortical activity during antagonist cocontraction and reciprocal inhibition of forearm muscles. J Neurophysiol 51: 32–49 Green MC (1981) Catalog of mutant genes and polymorphic loci. In: Green MC (ed) Genetic variants and strains of the laboratory mouse. Gustav Fisher Verlag, New York, pp 8–278 Grillner S, Hongo T, Lund S (1970) The vestibulospinal tract. Effects on alpha motoneurons in the lumbosacral spinal cord in the cat. Exp Brain Res 10: 94–120 Gruner JA, Altman J, Spirak N (1980) Effects of arrested cerebellar development on locomotion in the rat: cinematographic and electromyographic analysis. Exp Brain Res 40: 361–373 Martin MR, Caddy KWT (1977) Electrophysiological studies on interpositus neurones in the normal and Lurcher mutant mouse. Exp Brain Res 29: 275–281 Miller JG (1966) Simultaneous statistical inference. McGraw-Hill, New York Orlovsky GN (1970) Influence of the cerebellum on the reticulospinal neurones during locomotion. Biofizika 15: 894–901 Orlovsky GN (1972a) Work of the Purkinje cells during locomotion. Biofizika 17: 891–896 Orlovsky GN (1972b) Work of the neurones of the cerebellar nuclei during locomotion. Biofizika 17: 1119–1126 Orlovsky GN (1972c) Activity of vestibulospinal neurones during locomotion. Brain Res 46: 85–98 Orlovsky GN (1972d) Activity of rubrospinal neurons during locomotion. Brain Res 46: 99–112 Orlovsky GN, Severin FV, Shik ML (1966) Effect of damage to the cerebellum on the coordination of movement in the dog on running. Biofizika 11: 509–517 Philips RJS (1960) “Lurcher”. A new gene in linkage group XI of the house mouse. J Genet 57: 35–42 Rondot P, Bathien N, Toma S (1979) Physiopathology of cerebellar movement. In: Massion J, Sasaki K (eds) Cerebrocerebellar interactions. Elsevier/North Holland, Amsterdam, pp 203–230 Sidman RL, Green MC (1970) “Nervous”, a new mutant mouse with cerebellar disease. In: Sabourdy M (ed) Les mutants pathologiques chez l'animal. Centre National de la Recherche Scientifique, Paris, pp 69–79 Swisher DA, Wilson DB (1977) Cerebellar histogenesis in the Lurcher (Lc) mutant mouse. J Comp Neurol 173: 205–218 Udo M, Matsukawa K, Kamei H, Oda Y (1980) Cerebellar control of locomotion: effects of cooling cerebellar intermediate cortex in high decerebrate and awake walking cats. J Neurophysiol 44: 119–134 Udo M, Oda Y, Tanaka K, Horikawa J (1976) Cerebellar control of locomotion investigated in cats: discharges from Deiter's neurones, EMG and limb movements during local cooling of the cerebellar cortex. Prog Brain Res 44: 445–459 Wetts R, Herrup K (1982a) Interaction of granule, Purkinje and inferior olivary neurons in Lurcher chimeric mice. I. Qualitative studies. J Embryol Exp Morphol 68: 87–98 Wetts R, Herrup K (1982b) Cerebellar Purkinje cells are descended from a small number of progenitors committed during early development: quantitative analysis of Lurcher chimeric mice. J Neurosci 2: 1494–1498 Wetts R, Kalaska JF, Smith AM (1985) Cerebellar nuclear cell activity during antagonist cocontraction and reciprocal inhibition of forearm muscles. J Neurophysiol 54: 231–244 Yu J, Eidelberg E (1983) Recovery of locomotor function in cats after localized cerebellar lesions. Brain Res 273: 121–131