Deficiency of subunits of complex I or IV in mitochondrial myopathies: Immunochemical and immunohistochemical study

Journal of Inherited Metabolic Disease - Tập 10 Số 3 - Trang 284-288 - 1987
Tanaka, M.1, Nishikimi, M.1, Suzuki, H.1, Tada, M.1, Ozawa, T.1, Koga, Y.2, Nonaka, I.2
1Department of Biomedical Chemistry, Faculty of Medicine, University of Nagoya, Nagoya Japan
2National Institute of Neuroscience, NCNP, Kodaira, Tokyo Japan

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citation_journal_title=Trends Biochem. Sci.; citation_title=Organisation and expression of the mammalian mitochondrial genome: a lesson in economy; citation_author=G. Attardi; citation_volume=6; citation_publication_date=1981; citation_pages=86-89; citation_id=CR1 citation_journal_title=Biochim. Biophys. Acta; citation_title=Arrangement of proteins in the mitochondrial inner membrane; citation_author=R. A. Capaldi; citation_volume=694; citation_publication_date=1982; citation_pages=291-306; citation_id=CR2 citation_journal_title=Science; citation_title=URF6, last unidentified reading frame of human mtDNA, codes for an NADH dehydrogenase subunit; citation_author=A. Chomyn, M. W. J. Cleeter, C. I. Ragan, M. Riley, R. F. Doolittle, G. Attardi; citation_volume=234; citation_publication_date=1986; citation_pages=614-618; citation_id=CR3 citation_journal_title=Muscle Nerve; citation_title=Immunocytochemical demonstration of cytochromec oxidase and Complex III in tissues from patients with mitochondrial encephalopathy; citation_author=T. Sato, M. Anno, K. Arahata, S. Nakamura, M. Mukoyama, H. Nakamura, T. Ozawa; citation_volume=9; citation_publication_date=1986; citation_pages=183; citation_id=CR4 citation_journal_title=Biochem. Biophys. Res. Commun.; citation_title=Deficiency of subunits in heart mitochondrial NADH-ubiquinone oxidoreductase of a patient with mitochondrial encephalomyopathy and cardiomyopathy; citation_author=M. Tanaka, M. Nishikimi, H. Suzuki, T. Ozawa, M. Nishizawa, K. Tanaka, T. Miyatake; citation_volume=140; citation_publication_date=1986; citation_pages=88-93; citation_id=CR5 citation_journal_title=Ann. N.Y. Acad. Sci.; citation_title=Lack of subunit II of cytochromec oxidase in a patient with mitochondrial myopathy; citation_author=M. Tanaka, M. Nishikimi, T. Ozawa, S. Miyabayashi, K. Tada; citation_volume=488; citation_publication_date=1987; citation_pages=503-504; citation_id=CR6 citation_journal_title=Biochem. Int.; citation_title=Partial deficiency of subunits in Complex I or IV of patients with mitochondrial myopathies; citation_author=M. Tanaka, M. Nishikimi, H. Suzuki, T. Ozawa, Y. Koga, I. Nonaka; citation_volume=14; citation_publication_date=1987; citation_pages=525-530; citation_id=CR7 citation_journal_title=Biochem. Int.; citation_title=Variation in the levels of Complex I subunits among tissues in a patient with mitochondrial encephalomyopathy and renal dysfunction; citation_author=M. Tanaka, M. Nishikimi, H. Suzuki, T. Ozawa, T. Ichiki, M. Kobayashi, Y. Wada; citation_volume=14; citation_publication_date=1987; citation_pages=735-739; citation_id=CR8