Arthrogryposis Multiplex Congenita

Ulrich Mennen1, Ann van Heest1, Mary-Beth Ezaki1, Michael Tonkin1, George Gericke1
1From Pretoria, South Africa, Minnesota, USA, Texas, USA, Sydney, Australia and Pretoria, South Africa

Tóm tắt

Since much confusion exists regarding arthrogryposis multiplex congenita (AMC), the President of the IFSSH commissioned the AMC Committee to compile a report on the various aspects of this condition. This report discusses all the facets of AMC, including definition, terminology, dermographics, aetiology, classification, clinical features, management, prognosis and further studies. Manipulation of the deformities starting soon after birth improves the range of motion, which, if surgery needs to be done, makes the operation less extensive. Sometimes surgery may not even be necessary. Early one-stage corrective surgery between 3 and 12 months of age is encouraged. This results in improved function and near normal cosmetic appearance. Late, piece-meal surgery results in disappointing outcome.

Tài liệu tham khảo

10.1111/j.1399-0004.1984.tb00478.x James T, 1951, Medical Journal, 58, 565 10.1016/0266-7681(93)90046-I 10.1016/J.JHSB.2004.02.007 10.1016/S0266-7681(96)80150-1 Rocher HL, 1913, Journal de Médecine Bordeaux, 43, 772 SwaimanKFWrightFSThe practice of paediatric neurology199411St. LouisMosby Co116118 10.1016/S0363-5023(98)80017-8 AdamsRDDenny-BrownDPearsonCMDisease of muscle. A study in pathology1953New YorkPaul Hoeber229235 10.1302/0301-620X.52B3.483 Hall JG, 1981, Pediatric Annals, 10, 15 Hall JG, 1984, Birth Defects, 20, 8 10.1002/ajmg.1320110208 10.1002/ajmg.1320150407 10.1302/0301-620X.52B3.494 Otto AW, 1985, Clinical Orthopaedics and Related Research, 194, 4 10.2106/00004623-199072030-00027 10.2106/00004623-198264060-00024 10.1001/jama.1923.02650180025009 Swinyard CA, 1985, Clinical Orthopaedics and Related Research, 194, 15, 10.1097/00003086-198504000-00004 Williams P, 1978, Orthopaedic Clinics of North America, 9, 67, 10.1016/S0030-5898(20)30881-6 Wolf A, 1955, Neuropathology and Experimental Neurology, 14, 112 10.1136/adc.51.8.618