Retroperitoneal fibrosis and c-ANCA positivity

Clinical Rheumatology - Tập 26 - Trang 115-116 - 2005
Clio P. Mavragani1,2, Michalis Voulgarelis1
1Department of Pathophysiology, School of Medicine, National University of Athens, Athens, Greece
2Hospital for Special Surgery, New York, USA

Tóm tắt

Retroperitoneal fibrosis (RPF) is an uncommon collagen vascular disease characterized by a chronic nonspecific inflammation of the retroperitoneum, which can entrap and obstruct retroperitoneal structures. Although obscure, an autoimmune-mediated or vasculitic etiology has been hypothesized. In the current report, a case of RPF associated with the presence of antibodies against proteinase III, which responded effectively to immunosuppressive therapy, is presented.

Tài liệu tham khảo

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