Chiari I malformation, caudal regression syndrome, and Pierre Robin Syndrome: a previously unreported combination

Springer Science and Business Media LLC - Tập 22 - Trang 1507-1508 - 2006
R. Shane Tubbs1,2, W. Jerry Oakes2
1Department of Cell Biology, University of Alabama at Birmingham, Birmingham, USA
2Pediatric Neurosurgery, Children’s Hospital of Alabama, Birmingham, USA

Tóm tắt

The authors report a child born with a constellation of findings including Chiari I malformation, Pierre Robin syndrome, and caudal regression syndrome. In addition, this child was found to have a fatty-infiltrated filum terminale and a low conus medullaris. In isolation, the Chiari I malformation has been reported in patients with caudal regression and Pierre Robin syndrome. Speculation has been given to the possibility of a common insult to early mesodermal development and each of these pathological entities. To our knowledge, this is the first report of a single patient that possessed all three entities (i.e., Chiari I malformation, Pierre Robin syndrome, and caudal regression syndrome). Further case reports as this may shed light on the dysembryology that results in each of these diagnoses.

Tài liệu tham khảo

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