Familial double pericentric inversion of chromosome 5 with some features of cri-du-chat syndromeSpringer Science and Business Media LLC - Tập 97 - Trang 802-807 - 1996
Sheryl A. Goodart, Merlin G. Butler, Joan Overhauser
Fluorescence in situ hybridization analysis was performed to characterize a
complex pericentric inversion involving chromosome 5 in a mother and son. The
mother had hypertelorism, epicanthal folds, and mild mental deficiency while the
son had additional anomalies that have been observed in patients with
cri-du-chat syndrome. Both individuals were found to have an identical double
pericentric inver... hiện toàn bộ
Identification of ABCC6 pseudogenes on human chromosome 16p: implications for mutation detection in pseudoxanthoma elasticumSpringer Science and Business Media LLC - Tập 109 - Trang 356-365 - 2001
Leena Pulkkinen, Aoi Nakano, Franziska Ringpfeil, Jouni Uitto
Pseudoxanthoma elasticum (PXE), a heritable disorder affecting the skin, eyes,
and the cardiovascular system, has recently been linked to mutations in the
ABCC6 gene on chromosome 16p13.1. The original mutation detection strategy
employed by us consisted of the amplification of each exon of the ABCC6 gene
with primer pairs placed on the flanking introns, followed by heteroduplex
scanning and direc... hiện toàn bộ
Fortuitous detection of a sporadic carrier of Duchenne's muscular dystrophySpringer Science and Business Media LLC - Tập 6 - Trang 34-39 - 1968
James W. Hanson, Hans Zellweger, Adel K. Afifi, William F. McCormick
A case is presented of a 19-year-old white female, detected while we were
investigating the range of serum creatine kinase levels in “normal” controls.
She presented elevated serum creatine kinase, myopathic electromyogram, and
electron microscopic evidence of dystrophic changes in muscle tissue, but no
clinically detectable muscular weakness. The significance of these findings is
discussed. We fe... hiện toàn bộ
An effector index to predict target genes at GWAS lociSpringer Science and Business Media LLC - Tập 141 - Trang 1431-1447 - 2022
Vincenzo Forgetta, Lai Jiang, Nicholas A. Vulpescu, Megan S. Hogan, Siyuan Chen, John A. Morris, Stepan Grinek, Christian Benner, Dong-Keun Jang, Quy Hoang, Noel Burtt, Jason A. Flannick, Mark I. McCarthy, Eric Fauman, Celia M. T. Greenwood, Matthew T. Maurano, J. Brent Richards
Drug development and biological discovery require effective strategies to map
existing genetic associations to causal genes. To approach this problem, we
selected 12 common diseases and quantitative traits for which highly powered
genome-wide association studies (GWAS) were available. For each disease or
trait, we systematically curated positive control gene sets from Mendelian forms
of the diseas... hiện toàn bộ
Common 5′ β-globin RFLP haplotypes harbour a surprising level of ancestral sequence mosaicismSpringer Science and Business Media LLC - Tập 113 - Trang 123-139 - 2003
Matthew T. Webster, John B. Clegg, Rosalind M. Harding
Blocks of linkage disequilibrium (LD) in the human genome represent segments of
ancestral chromosomes. To investigate the relationship between LD and genealogy,
we analysed diversity associated with restriction fragment length polymorphism
(RFLP) haplotypes of the 5′ β-globin gene complex. Genealogical analyses were
based on sequence alleles that spanned a 12.2-kb interval, covering 3.1 kb
around ... hiện toàn bộ
Isoenzymes and population genetics of sorbit dehydrogenase (EC: 1.1.1.14) in swine (sus scrofa)Springer Science and Business Media LLC - Tập 7 - Trang 258-259 - 1969
J. Op't Hof
A method is described for detecting the enzyme sorbit dehydrogenase (SDH) after
starchgel electrophoresis. Activity of this enzyme occurs predominantly in
liver, kidney, thyroid and testis. It was found that this enzyme exists in
multiple molecular forms. Three electrophoretic phenotypes were observed
apparently representing two different homozygotes and the corresponding
heterozygote. These findi... hiện toàn bộ