Why, when and how to investigate primary ciliary dyskinesia in adult patients with bronchiectasis

Mattioli1885 - Tập 13 Số S1 - 2018
Martina Contarini1, Amelia Shoemark2, Jessica Rademacher3, Simon Finch2, Andrea Gramegna1, Michele Gaffuri4, L. Roncoroni4, Manuela Seia5, Felix C. Ringshausen3, Tobias Welte3, Francesco Blasi1, Stefano Aliberti1, James D. Chalmers2
1Department of Pathophysiology and Transplantation, University of Milan, Internal Medicine Department, Respiratory unit and Adult Cystic Fibrosis Center, Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Via Francesco Sforza 35, 20122, Milan, Italy
2Division of Molecular and Clinical Medicine, University of Dundee, Ninewells Hospital and Medical School, Dundee, UK
3Department of Respiratory Medicine, Hannover Medical School and German Center for Lung Research (DZL), Hannover, Germany
4Department of Otolaryngology and Head and Neck Surgery, Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Department of Clinical Sciences and Community Health, University of Milan, Milan, Italy
5Medical Genetics Laboratory, Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Milan, Italy

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