The role of radiotherapy in 74 patients with dermatofibrosarcoma protuberans

Springer Science and Business Media LLC - Tập 5 - Trang 454-457 - 2006
Xiushen Wang1, Mengzhong Liu2, Hui Liu2, Nianji Cui2
1Department of Radiotherapy, Cancer Hospital of Henan Province, Zhengzhou, China
2Department of Radiotherapy, Cancer Hospital, Sun Yat-sen University, Guangzhou, China

Tóm tắt

To study treatment and prognostic factor in 74 patients with dermatofibrosarcoma protuberans. From August 1990 to November 1999, 74 patients with dermatofibrosarcoma protuberans (DFSP) confirmed by pathology were treated in Cancer Hospital of Sun Yat-sen University. 72 cases were given wide excision and 2 cases were given local excision. All of 74 cases, 52 cases had surgical resection alone, and 22 cases had surgical resection combined with radiotherapy. Total dose of radiotherapy was 50–70 Gy. The rate of recurrence was 36.1% for all patients. The 5-year recurrence-free survival (RFS) rate was 66%. The 5-year recurrence-free survival rates for resection alone and combined with radiotherapy were 58% and 90%, respectively (P=0.0187). The 5-year recurrence-free survival rates for positive microscopic margins and negative microscopic margins were 57% and 75%, respectively (P=0.0468). Post-operation radiotherapy is an effective treatment to decrease the recurrence rate for the patients with positive microscope, or the patients without suitable surgical treatment.

Tài liệu tham khảo

Taylor HB, Helwig EB. Dermatofibrosarcoma protuberans. A study of 115 cases. Cancer, 1962, 15: 717–725. Mcpeak CJ, Cruz T, Nicastri AD. Dermatofibrosarcoma protuberans: an analysis of 86 cases — five with metastasis. Ann Surg, 1967, 166: 803–816. Mentzel T, Beham A, Katenkamp D, et al. Fibrosarcomatous (high-grade) dermatofibrosarcoma protuberans: clinicopathologic and immunohistochemical study of a series of 41 cases with emphasis on prognostic significance. Am J Surg Pathol, 1998, 22: 576–587. Suit H, Spiro I, Mankin HJ, et al. Radiation in management of patients with dermatofibrosarcoma protuberans. J Clin Oncol, 1996, 14: 2365–2369. Haas RL, Keus RB, Loftus BM, et al. The role of radiotherapy in the local management of dermatofibrosarcoma protuberans. Eur J Cancer, 1997, 33: 1055–1060. Ballo MT, Zagars GK, Pisters P, et al. The role of radiation therapy in the management of dermatofibrosarcoma protuberans. Int J Radiat Oncol Biol Phys, 1998, 40: 823–827. Bowne WB, Antonescu CR, Leung DH, et al. Dermatofibrosarcoma protuberans: a clinicopathologic analysis of patients treated and followed at a single institution. Cancer, 2000, 88: 2711–2720. Ding J, Hashimoto H, Enjoji M, et al. Dermatofibrosarcoma protuberans with fibrosarcomatous areas. A clinicopathologic study of nine cases and a comparison with allied tumors. Cancer, 1989, 64: 721–729. Pack GT, Tabah EJ. Dermato-fibrosarcoma protuberans: a report of 39 cases. AMA Arch Surg, 1951, 62: 391–411. Linder NJ, Scarborough MT, Powell GJ, et al. Revision surgery in dermatofibrosarcoma protuberans of the trunk and extremities. Eur J Surg Oncol, 1999, 25: 392–397. Roses DF, Valensi Q, LaTrenta G, et al. Surgical treatment of dermatofibrosarcoma protuberans. Surg Gynecol Obstet, 1986, 162: 449–452. Hobbs ER, Wheeland RG, Bailin PL, et al. Treatment of dermatofibrosarcoma protuberans with Mohs micrographic surgery. Ann Surg, 1988, 207: 102–107.