The “normal” factor VIII concentration in plasma

Barrowcliffe, 2002, Coagulation and chromogenic assays of factor VIII activity: general aspects, standardization, and recommendations, Semin Thromb Hemost, 28, 247, 10.1055/s-2002-32658 Lundblad, 2000, Issues with the assay of factor VIII activity in plasma and factor VIII concentrates, Thromb Haemost, 84, 942, 10.1055/s-0037-1614153 Hubbard, 2003, A multi-centre collaborative study on the potency estimation of ReFacto, Thromb Haemost, 90, 1088, 10.1160/TH03-02-0082 Butenas, 2009, The influence of von Willebrand factor on factor VIII activity measurements, J Thromb Haemost, 7, 132, 10.1111/j.1538-7836.2008.03210.x Chandler, 2003, Comparison of three methods for measuring factor VIII levels in plasma, Am J Clin Pathol, 120, 34, 10.1309/C8T8YNB4G3W45PRF Cinotti, 1991, Reproducibility of one-stage, two-stage and chromogenic assays of factor VIII activity: a multi-center study, Thromb Res, 61, 385, 10.1016/0049-3848(91)90652-D Hubbard, 2001, Potency estimation of recombinant factor VIII: effect of assay method and standard, Br J Haematol, 113, 533, 10.1046/j.1365-2141.2001.02761.x Ingerslev, 2004, Collaborative field study on the utility of a BDD factor VIII concentrate standard in the estimation of BDDr Factor VIII:C activity in hemophilic plasma using one-stage clotting assays, J Thromb Haemost, 2, 623, 10.1111/j.1538-7836.2004.00657.x Rodgers, 2007, In vitro kinetics of factor VIII activity in patients with mild haemophilia A and a discrepancy between one-stage and two-stage factor VIII assay results, Br J Haematol, 136, 138, 10.1111/j.1365-2141.2006.06402.x Morfini, 2003, A multicenter pharmacokinetic study of the B-domain deleted recombinant factor VIII concentrate using different assays and standards, J Thromb Haemost, 1, 2283, 10.1046/j.1538-7836.2003.00481.x Raut, 2003, Variability in factor VIII concentrate measurement: results from SSC field collaborative studies, J Thromb Haemost, 1, 1927, 10.1046/j.1538-7836.2003.00342.x Lollar, 1988, Association of the factor VIII light chain with von Willebrand factor, J Biol Chem, 263, 10451, 10.1016/S0021-9258(19)81537-5 Hamer, 1987, Factor VIII binds to von Willebrand factor via its Mr-80, 000 light chain, Eur J Biochem, 166, 37, 10.1111/j.1432-1033.1987.tb13480.x Tuddenham, 1982, Response to infusions of polyelectrolyte fractionated human factor VIII concentrate in human haemophilia A and von Willebrand's disease, Br J Haematol, 52, 259, 10.1111/j.1365-2141.1982.tb03888.x Fass, 1975, Stability of porcine factor VIII, Thromb Res, 6, 109, 10.1016/0049-3848(75)90016-X Muntean, 1982, Influence of high molecular weight factor VIII on the measurement of low molecular weight factor VIII procoagulant in different assay systems, Br J Haematol, 51, 649, 10.1111/j.1365-2141.1982.tb02829.x Butenas, 2009, Potency and mass of factor VIII in FVIII products, Haemophilia, 15, 63, 10.1111/j.1365-2516.2008.01826.x Precup, 1991, A monoclonal antibody to factor VIII inhibits von Willebrand factor binding and thrombin cleavage, Blood, 77, 1929, 10.1182/blood.V77.9.1929.1929 Fay, 1989, Intersubunit fluorescence energy transfer in human factor VIII, J Biol Chem, 264, 14005, 10.1016/S0021-9258(18)71633-5 Lollar, 1993, Factor VIII and factor VIIIa, Methods Enzymol, 222, 128, 10.1016/0076-6879(93)22010-D Krudysz-Amblo, 2009, Quantitation of anti-factor VIII antibodies in human plasma, Blood, 113, 2587, 10.1182/blood-2008-08-174987 Hoyer, 1981, The factor VIII complex: structure and function, Blood, 58, 1, 10.1182/blood.V58.1.1.1 Lollar, 1984, Stabilization of thrombin-activated porcine factor VIII:C by factor IXa phospholipid, Blood, 63, 1303, 10.1182/blood.V63.6.1303.1303 De Visser, 2003, Linkage analysis of factor VIII and von Willebrand factor loci as quantitative trait loci, J Thromb Haemost, 1, 1771, 10.1046/j.1538-7836.2003.00314.x Souto, 2000, Functional effects of the ABO locus polymorphism on plasma levels of von Willebrand factor, factor VIII, and activated partial thromboplastin time, Arterioscler Thromb Vasc Biol, 20, 2024, 10.1161/01.ATV.20.8.2024 O'Donnell, 2000, Elevation of FVIII: C in venous thromboembolism is persistent and independent of the acute phase response, Thromb Haemost, 83, 10, 10.1055/s-0037-1613748 Vidal, 2001, Rapid hemophilia A molecular diagnosis by a simple DNA sequencing procedure: identification of 14 novel mutations, Thromb Haemost, 85, 580, 10.1055/s-0037-1615637