The Human Cytochrome c Oxidase Assembly Factors SCO1 and SCO2 Have Regulatory Roles in the Maintenance of Cellular Copper Homeostasis

Cell Metabolism - Tập 5 Số 1 - Trang 9-20 - 2007
Scot C. Leary1,2, Paul A. Cobine3, Brett A. Kaufman1,2, Guy-Hellen Guercin1,2, Andre Mattman4, Jan Palaty4, Gillian Lockitch4, Dennis R. Winge3, Pierre Rustin5, Rita Horváth6, Eric A. Shoubridge1,2
1Department of Human Genetics, McGill University, Montreal, QC H3A 2B4, Canada
2Montreal Neurological Institute, McGill University, Montreal, QC H3A 2B4, Canada
3Department of Medicine and Department of Biochemistry, University of Utah Health Sciences Center, Salt Lake City, UT 84132, USA
4Department of Pathology and Laboratory Medicine, Children's & Women's Health Centre of British Columbia, Vancouver, BC V6H 3N1, Canada
5Faculty of Medicine Denis Diderot, INSERM U676 and University of Paris 7, 75019 Paris, France
6Metabolic Disease Centre Munich-Schwabing and Institute of Clinical Chemistry, Molecular Diagnostics and Mitochondrial Genetics, 80804 Munich, Germany

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