Risk-Stratified Approach to Hybrid Transcatheter–Surgical Palliation of Hypoplastic Left Heart Syndrome

Pediatric Cardiology - Tập 27 - Trang 91-95 - 2006
D.S. Lim1, B.B. Peeler2, G.P. Matherne1, I.L. Kron2, H.P. Gutgesell1
1Children’s Hospital Heart Center, Department of Pediatrics, University of Virginia, Charlottesville, USA
2Children’s Hospital Heart Center, Department of Surgery, University of Virginia, Charlottesville, USA

Tóm tắt

We prospectively employed a risk-stratified approach to first-stage palliation of hypoplastic left heart syndrome. High-risk features included severe tricuspid insufficiency, severe right ventricular dysfunction, a severely restrictive or intact atrial septum, an ascending aortic diameter ≤2 mm, late presentation, weight <2 kg, or significant extracardiac issues, Infants without high-risk features underwent a Norwood procedure (with Sano modification), whereas infants with high-risk features underwent a hybrid procedure consisting of bilateral pulmonary artery banding, ductal stenting, and atrial septostomy or a Norwood/Sano. Operative survival for 10 infants without high-risk features undergoing a Norwood/Sano procedure was 90%. Operative survival for 5 infants with high-risk features undergoing hybrid palliation was 100%, compared to 29% in 7 infants with high-risk features undergoing the Norwood/Sano procedure. Although only short-term data are available, this hybrid palliative procedure may have a role for infants with hypoplastic left heart syndrome and high-risk features.

Tài liệu tham khảo

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