Radioembolization for Hepatocellular Carcinoma Arising in the Setting of a Congenital Extrahepatic Portosystemic Shunt (Abernethy Malformation)

Springer Science and Business Media LLC - Tập 41 - Trang 1285-1290 - 2018
Thomas Kroencke1, Marcus Murnauer2, Frank Alexander Jordan3, Vera Blodow4, Hannes Ruhnke1, Tina Schaller5, Bruno Märkl5
1Department of Diagnostic and Interventional Radiology and Neuroradiology, Klinikum Augsburg, Augsburg, Germany
2Department of General, Visceral and Transplant Surgery, Klinikum Augsburg, Augsburg, Germany
3Department of Medical Oncology, Klinikum Augsburg, Augsburg, Germany
4Department of Nuclear Medicine, Klinikum Augsburg, Augsburg, Germany
5Institute of Pathology, Klinikum Augsburg, Augsburg, Germany

Tóm tắt

In a 50-year-old male with an incidentally discovered hepatocellular carcinoma, a congenital extrahepatic portosystemic shunt with the absence of the portal vein (Abernethy syndrome) was diagnosed by imaging. This study aims to discuss the variant anatomy relevant to this splanchnic vascular malformation, review its association with the development of liver neoplasms, and report the safety and efficacy of TARE followed by resection for a HCC arising in this rare condition.

Tài liệu tham khảo

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