Bệnh Prion — Chúng đóng vai trò gì ngày nay?

InFo Neurologie & Psychiatrie - Tập 15 Số 6 - Trang 42-49 - 2013
Ponto, Claudia1, Zerr, Inga1
1Prionforschungsgruppe Neurologische Klinik, Universitätsmedizin, Göttingen, Deutschland

Tóm tắt

Khái niệm về sự sai lệch cấu trúc protein như một nguyên nhân gây thoái hóa thần kinh, chẳng hạn như bệnh Creutzfeldt-Jakob (CJK), lần đầu tiên được mô tả trong nhóm các bệnh prion. Mặc dù được coi là tương đối hiếm và kỳ lạ, chúng cuối cùng đã đóng vai trò lớn trong việc hiểu các cơ chế bệnh sinh trong các bệnh thoái hóa thần kinh khác.

Từ khóa

#Bệnh prion #thoái hóa thần kinh #bệnh Creutzfeldt-Jakob #cơ chế bệnh sinh.

Tài liệu tham khảo

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