Long-Chain Acyl-CoA Profiles in Cultured Fibroblasts from Patients with Defects in Fatty Acid Oxidation

Biochemical and Molecular Medicine - Tập 55 - Trang 15-21 - 1995
C.S. Tamvakopoulos1, S. Willi1, V.E. Anderson1, D.E. Hale1
1Brown Univ, Dept Chem, Providence, RI 02912, USA and Childrens Hosp, Div Endocrinol & Diabet, Philadelphia, PA 19104, USA