Fibrillins

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XXII. The complete sequences of 100 new cDNA clones from brain which code for large proteins in vitro, DNA Research, 8, 85, 10.1093/dnares/8.2.85 Neptune, 2003, Dysregulation of TGF-beta activation contributes to pathogenesis in Marfan syndrome, Nature Genetics, 33, 407, 10.1038/ng1116 Pereira, 1993, Genomic organization of the sequence coding for fibrillin, the defective gene product in Marfan syndrome, Human Molecular Genetics, 2, 961, 10.1093/hmg/2.7.961 Pfaff, 1996, Cell adhesion and integrin binding to recombinant human fibrillin-1, FEBS Letters, 384, 247, 10.1016/0014-5793(96)00325-0 Pyeritz, 2002, Marfan syndrome and other microfibrillar disorders, 585 Qian, 1997, Alignment of fibrillin molecules in elastic microfibrils is defined by transglutaminase-derived cross-links, Biochemistry, 36, 15841, 10.1021/bi971036f Reinhardt, 1996, Fibrillin 1: Organization in microfibrils and structural properties, Journal of Molecular Biology, 258, 104, 10.1006/jmbi.1996.0237 Reinhardt, 1997, Calcium determines the shape of fibrillin, The Journal of Biological Chemistry, 272, 7368, 10.1074/jbc.272.11.7368 Reinhardt, 1997, Calcium stabilizes fibrillin-1 against proteolytic degradation, The Journal of Biological Chemistry, 272, 1231, 10.1074/jbc.272.2.1231 Ritty, 1999, Processing of the fibrillin-1 carboxyl-terminal domain, The Journal of Biological Chemistry, 274, 8933, 10.1074/jbc.274.13.8933 Robinson, 2006, The molecular genetics of Marfan syndrome and related disorders, Journal of Medical Genetics, 43, 769, 10.1136/jmg.2005.039669 Rock, 2004, Molecular basis of elastic fiber formation. Critical interactions and a tropoelastin-fibrillin-1 cross-link, The Journal of Biological Chemistry, 279, 23748, 10.1074/jbc.M400212200 Sabatier, 2009, Fibrillin assembly requires fibronectin, Molecular Biology of the Cell, 20, 846, 10.1091/mbc.e08-08-0830 Sabatier, 2013, Complex contributions of fibronectin to initiation and maturation of microfibrils, Biochemical Journal, 456, 283, 10.1042/BJ20130699 Sabatier, 2014, Heparin/heparan sulfate controls fibrillin-1, -2 and -3 self-interactions in microfibril assembly, FEBS Letters, 588, 2890, 10.1016/j.febslet.2014.06.061 Sakai, 1991, Purification and partial characterization of fibrillin, a cysteine-rich structural component of connective tissue microfibrils, The Journal of Biological Chemistry, 266, 14763, 10.1016/S0021-9258(18)98752-1 Sakamoto, 1996, Cell-type specific recognition of RGD- and non-RGD-containing cell binding domains in fibrillin-1, The Journal of Biological Chemistry, 271, 4916, 10.1074/jbc.271.9.4916 Tangemann, 1995, Demonstration of non-linear detection in ELISA resulting in up to 1000-fold too high affinities of fibrinogen binding to integrin alpha IIb beta 3, FEBS Letters, 358, 179, 10.1016/0014-5793(94)01411-S Tiedemann, 2001, Interactions of fibrillin-1 with heparin/heparan sulfate: Implications for microfibrillar assembly, The Journal of Biological Chemistry, 276, 36035, 10.1074/jbc.M104985200 Trask, 1999, N-terminal domains of fibrillin 1 and fibrillin 2 direct the formation of homodimers: A possible first step in microfibril assembly, Biochemical Journal, 340, 693, 10.1042/bj3400693 Wagenseil, 2007, New insights into elastic fiber assembly, Birth Defects Research.Part C, Embryo Today, 81, 229, 10.1002/bdrc.20111 Wallis, 2003, Profibrillin-1 maturation by human dermal fibroblasts: Proteolytic processing and molecular chaperones, Journal of Cellular Biochemistry, 90, 641, 10.1002/jcb.10657 Werner, 2000, Backbone dynamics of a cbEGF domain pair in the presence of calcium, Journal of Molecular Biology, 296, 1065, 10.1006/jmbi.1999.3513 Zhang, 1994, Structure and expression of fibrillin-2, a novel microfibrillar component preferentially located in elastic matrices, Journal of Cell Biology, 124, 855, 10.1083/jcb.124.5.855