Ectopically Expressed CAG Repeats Cause Intranuclear Inclusions and a Progressive Late Onset Neurological Phenotype in the Mouse

Cell - Tập 91 - Trang 753-763 - 1997
Jared M Ordway1, Sara Tallaksen-Greene2, Claire-Anne Gutekunst3, Eve M Bernstein4, Jamie A Cearley1, Howard W Wiener5, Leon S Dure6, Russell Lindsey7, Steven M Hersch3, Richard S Jope4, Roger.L Albin2, Peter J Detloff1
1Department of Biochemistry and Molecular Genetics, University of Alabama at Birmingham, Birmingham, Alabama 35294, USA
2Department of Neurology University of Michigan, Ann Arbor, Michigan 48104 USA
3Department of Neurology, Emory University, Atlanta, Georgia 30329, USA
4Department of Psychiatry and Behavioral Neurobiology, University of Alabama at Birmingham, Birmingham, Alabama 35294, USA
5Department of Oral Biology, University of Alabama at Birmingham, Birmingham, Alabama 35294, USA
6Department of Pediatric Neurology, University of Alabama at Birmingham, Birmingham, Alabama 35294, USA
7Department of Comparative Medicine, University of Alabama at Birmingham, Birmingham, Alabama 35294 USA

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