Current concepts and controversy in chronic inflammatory demyelinating polyneuropathy

Current Neurology and Neuroscience Reports - Tập 3 Số 1 - Trang 57-63 - 2003
Saperstein, David S.1, Barohn, Richard J.1
1Department of Neurology, The University of Kansas Medical Center, Kansas City, USA

Tóm tắt

Chronic inflammatory demyelinating polyneuropathy (CIDP) is an acquired, immune-mediated demyelinating neuropathy. It is the most common treatable acquired polyneuropathy and represents a significant number of initially undiagnosed neuropathy patients. This article reviews the common clinical, laboratory, and electrodiagnostic features of CIDP. In addition, current areas of uncertainty are discussed.

Tài liệu tham khảo

citation_journal_title=Mayo Clin Proc; citation_title=Chronic inflammatory polyradiculoneuropathy; citation_author=PJ Dyck, AC Lais, M Ohta; citation_volume=50; citation_publication_date=1975; citation_pages=621-637; citation_id=CR1 citation_journal_title=Arch Neurol; citation_title=Chronic inflammatory demyelinating polyradiculoneuropathy. Clinical characteristics, course, and recommendations for diagnostic criteria; citation_author=RJ Barohn, JT Kissel, JR Warmolts, JR Mendell; citation_volume=46; citation_publication_date=1989; citation_pages=878-884; citation_id=CR2 citation_journal_title=J Neurol Sci; citation_title=Age of onset influences clinical features of chronic inflammatory demyelinating polyneuropathy; citation_author=N Hattori, K Misu, H Koike; citation_volume=184; citation_publication_date=2000; citation_pages=57-63; citation_doi=10.1016/S0022-510X(00)00493-7; citation_id=CR3 citation_journal_title=Neurology; citation_title=Chronic inflammatory demyelinating polyneuropathy: clinical features and response to treatment in 67 consecutive patients with and without a monoclonal gammopathy; citation_author=KC Gorson, G Allam, AH Ropper; citation_volume=48; citation_publication_date=1997; citation_pages=321-328; citation_id=CR4 citation_journal_title=J Neurol; citation_title=Pure motor chronic inflammatory demyelinating polyneuropathy; citation_author=M Sabatelli, F Madia, T Mignogna; citation_volume=248; citation_publication_date=2001; citation_pages=772-777; citation_doi=10.1007/s004150170093; citation_id=CR5 citation_journal_title=J Neurol Sci; citation_title=Chronic relapsing polyneuritis; citation_author=JW Prineas, JG McLeod; citation_volume=27; citation_publication_date=1976; citation_pages=427-458; citation_doi=10.1016/0022-510X(76)90213-6; citation_id=CR6 citation_journal_title=Neurology; citation_title=Micturitional disturbance in patients with chronic inflammatory demyelinating polyneuropathy; citation_author=R Sakakibara, T Hattori, S Kuwabara; citation_volume=50; citation_publication_date=1998; citation_pages=1179-1182; citation_id=CR7 citation_journal_title=Ann Neurol; citation_title=Guillain-Barré syndrome and chronic inflammatory demyelinating polyneuropathy: immune mechanisms and update on current therapies; citation_author=FG Meche, PA Doorn; citation_volume=37; citation_issue=suppl 1; citation_publication_date=1995; citation_pages=S14-S31; citation_doi=10.1002/ana.410370704; citation_id=CR8 citation_journal_title=Neurology; citation_title=Research criteria for diagnosis of chronic inflammatory demyelinating polyneuropathy (CIDP). Report from an Ad Hoc Subcommittee of the American Academy of Neurology AIDS Task Force; citation_author=; citation_volume=41; citation_publication_date=1991; citation_pages=617-618; citation_id=CR9 citation_journal_title=Neurology; citation_title=CSF "monoclonal" bands in chronic relapsing polyneuropathy; citation_author=M Dalakas, SA Houff, WK Engel, DL Madden, JL Sever; citation_volume=30; citation_publication_date=1980; citation_pages=864-867; citation_id=CR10 citation_journal_title=Neuromusc Disord; citation_title=Neuropathies associated with monoclonal proteins; citation_author=JT Kissel, JR Mendell; citation_volume=6; citation_publication_date=1995; citation_pages=3-18; citation_doi=10.1016/0960-8966(95)00021-6; citation_id=CR11 citation_journal_title=Muscle Nerve; citation_title=Acquired inflammatory demyelinating polyneuropathies: clinical and electrodiagnostic features; citation_author=JW Albers, JJ Kelly; citation_volume=12; citation_publication_date=1989; citation_pages=435-451; citation_doi=10.1002/mus.880120602; citation_id=CR12 citation_journal_title=Muscle Nerve; citation_title=Comparison of electrodiagnostic criteria for primary demyelination in chronic polyneuropathy; citation_author=MB Bromberg; citation_volume=14; citation_publication_date=1991; citation_pages=968-976; citation_doi=10.1002/mus.880141007; citation_id=CR13 citation_journal_title=J Neurol Sci; citation_title=The spectrum of chronic inflammatory demyelinating polyneuropathy; citation_author=FT Rotta, AT Sussman, WG Bradley; citation_volume=173; citation_publication_date=2000; citation_pages=129-139; citation_doi=10.1016/S0022-510X(99)00317-2; citation_id=CR14 citation_journal_title=Ann Neurol; citation_title=A computer simulation of conduction block: effects produced by actual block versus interphase cancellation; citation_author=EK Rhee, JD England, AJ Sumner; citation_volume=28; citation_publication_date=1990; citation_pages=146-156; citation_doi=10.1002/ana.410280206; citation_id=CR15 citation_journal_title=Muscle Nerve; citation_title=What is the best diagnostic index of conduction block and temporal dispersion; citation_author=SJ Oh, DE Kim, AR Koruoglu; citation_volume=17; citation_publication_date=1994; citation_pages=489-493; citation_doi=10.1002/mus.880170504; citation_id=CR16 citation_journal_title=Muscle Nerve; citation_title=Conduction block in clinical practice; citation_author=DR Cornblath, AJ Sumner, J Daube; citation_volume=14; citation_publication_date=1991; citation_pages=869-871; citation_doi=10.1002/mus.880140913; citation_id=CR17 citation_journal_title=Muscle Nerve; citation_title=Consensus criteria for the diagnosis of partial conduction block; citation_author=RK Olney; citation_volume=22; citation_issue=suppl 8; citation_publication_date=1999; citation_pages=S225-S229; citation_id=CR18 citation_journal_title=J Neurol Neurosurg Psychiatry; citation_title=Diagnostic value of sural nerve biopsy in chronic inflammatory demyelinating polyneuropathy; citation_author=DS Molenaar, M Vermeulen, R Haan; citation_volume=64; citation_publication_date=1998; citation_pages=84-89; citation_doi=10.1136/jnnp.64.1.84; citation_id=CR19 citation_journal_title=Brain; citation_title=Diagnostic value of sural demyelination in chronic inflammatory demyelinating polyneuropathy; citation_author=WM Bosboom, LH Berg, H Franssen; citation_volume=124; citation_publication_date=2001; citation_pages=2427-2438; citation_doi=10.1093/brain/124.12.2427; citation_id=CR20 citation_journal_title=Ann Neurol; citation_title=Prednisone improves chronic inflammatory demyelinating polyradiculoneuropathy more than no treatment; citation_author=PJ Dyck, PC O’Brien, KF Oviatt; citation_volume=11; citation_publication_date=1982; citation_pages=136-141; citation_doi=10.1002/ana.410110205; citation_id=CR21 citation_journal_title=N Engl J Med; citation_title=Plasma exchange in chronic inflammatory demyelinating polyradiculoneuropathy; citation_author=PJ Dyck, J Daube, P O’Brien; citation_volume=314; citation_publication_date=1986; citation_pages=461-465; citation_doi=10.1056/NEJM198602203140801; citation_id=CR22 citation_journal_title=Brain; citation_title=Plasma-exchange therapy in chronic inflammatory demyelinating polyneuropathy: a double-blind, sham-controlled, cross-over study; citation_author=AF Hahn, CF Bolton, N Pillay; citation_volume=119; citation_publication_date=1996; citation_pages=1055-1066; citation_doi=10.1093/brain/119.4.1055; citation_id=CR23 citation_journal_title=Brain; citation_title=Intravenous immunoglobulin treatment in chronic inflammatory demyelinating polyneuropathy: a double-blind, placebocontrolled, cross-over study; citation_author=AF Hahn, CF Bolton, D Zochodne, TE Feasby; citation_volume=119; citation_publication_date=1996; citation_pages=1067-1077; citation_doi=10.1093/brain/119.4.1067; citation_id=CR24 citation_journal_title=Neurology; citation_title=Randomized controlled trial of IVIg in untreated chronic inflammatory demyelinating polyradiculoneuropathy; citation_author=JR Mendell, RJ Barohn, ML Freimer; citation_volume=56; citation_publication_date=2001; citation_pages=445-449; citation_id=CR25 citation_journal_title=Ann Neurol; citation_title=Randomized controlled trial of intravenous immunoglobulin versus oral prednisolone in chronic inflammatory demyelinating polyradiculoneuropathy; citation_author=R Hughes, S Bensa, H Willison; citation_volume=50; citation_publication_date=2001; citation_pages=195-201; citation_doi=10.1002/ana.1088; citation_id=CR26 citation_journal_title=Neurology; citation_title=Combined azathioprine and prednisone in chronic inflammatory demyelinating polyneuropathy; citation_author=PJ Dyck, P O’Brien, C Swanson, P Low, J Daube; citation_volume=35; citation_publication_date=1985; citation_pages=1173-1176; citation_id=CR27 citation_journal_title=Muscle Nerve; citation_title=Cyclosporine A in resistant chronic inflammatory demyelinating polyradiculoneuropathy; citation_author=MH Barnett, JD Pollard, L Davies, JG McLeod; citation_volume=21; citation_publication_date=1998; citation_pages=454-460; citation_doi=10.1002/(SICI)1097-4598(199804)21:4<454::AID-MUS3>3.0.CO;2-8; citation_id=CR28 citation_journal_title=J Neurol Neurosurg Psychiatry; citation_title=Cyclosporin A in the treatment of chronic demyelinating polyradiculoneuropathy; citation_author=SJ Hodgkinson, JD Pollard, JG McLeod; citation_volume=53; citation_publication_date=1990; citation_pages=327-330; citation_id=CR29 citation_journal_title=Neurology; citation_title=Pulsed cyclophosphamide in chronic inflammatory demyelinating polyneuropathy; citation_author=JL Good, M Chehrenama, RF Mayer, CL Koski; citation_volume=51; citation_publication_date=1998; citation_pages=1735-1738; citation_id=CR30 citation_journal_title=Neurology; citation_title=High-dose cyclophosphamide without stem-cell rescue for refractory CIDP; citation_author=TH Brannagan, A Pradham, T Heiman-Patterson; citation_volume=58; citation_publication_date=2002; citation_pages=1856-1858; citation_id=CR31 citation_journal_title=J Neurol Neurosurg Psychiatry; citation_title=Interferon-alpha may benefit steroid unresponsive chronic inflammatory demyelinating polyneuropathy; citation_author=M Sabatelli, T Mignogna, G Lippi; citation_volume=58; citation_publication_date=1995; citation_pages=638-639; citation_id=CR32 citation_journal_title=Neurology; citation_title=Treatment of chronic inflammatory demyelinating polyneuropathy with interferon-alpha 2a; citation_author=KC Gorson, AH Ropper, BD Clark; citation_volume=50; citation_publication_date=1998; citation_pages=84-87; citation_id=CR33 citation_journal_title=J Neurol Sci; citation_title=Mycophenolate (CellCept) treatment of myasthenia gravis, chronic inflammatory polyneuropathy and inclusion body myositis; citation_author=N Mowzoon, A Sussman, WG Bradley; citation_volume=185; citation_publication_date=2001; citation_pages=119-122; citation_doi=10.1016/S0022-510X(01)00478-6; citation_id=CR34 citation_journal_title=Neurology; citation_title=Mycophenolate mofetil: a safe and promising immunosuppressant in neuromuscular diseases; citation_author=V Chaudhry, DR Cornblath, JW Griffin, R O’Brien, DB Drachman; citation_volume=56; citation_publication_date=2001; citation_pages=94-96; citation_id=CR35 citation_journal_title=Muscle Nerve; citation_title=Clinical spectrum of chronic acquired demyelinating polyneuropathies; citation_author=DS Saperstein, JS Katz, AA Amato, RJ Barohn; citation_volume=24; citation_publication_date=2001; citation_pages=311-324; citation_doi=10.1002/1097-4598(200103)24:3<311::AID-MUS1001>3.0.CO;2-A; citation_id=CR36 citation_title=Neuropathy associated with the monoclonal gammopathies; citation_inbook_title=Peripheral Neuropathy; citation_publication_date=1993; citation_pages=1275-1287; citation_id=CR37; citation_author=RA Kyle; citation_author=PJ Dyck; citation_publisher=WB Saunders citation_journal_title=Neurology; citation_title=Distal acquired demyelinating symmetrical neuropathy; citation_author=JS Katz, DS Saperstein, GS Gronseth, AA Amato, RJ Barohn; citation_volume=54; citation_publication_date=2000; citation_pages=615-620; citation_id=CR38 citation_journal_title=Neurology; citation_title=Presentation and initial clinical course in patients with chronic inflammatory demyelinating polyradiculoneuropathy: comparison of patients without and with monoclonal gammopathy; citation_author=Z Simmons, JW Albers, MB Bromberg, EL Feldman; citation_volume=43; citation_publication_date=1993; citation_pages=2202-2209; citation_id=CR39 citation_journal_title=Brain; citation_title=Long-term prognosis of neuropathy associated with anti-MAG IgM M-proteins and its relationship to immune therapies; citation_author=E Nobile-Orazio, N Meucci, L Baldini, A Troia, G Scarlato; citation_volume=123; citation_publication_date=2000; citation_pages=710-717; citation_doi=10.1093/brain/123.4.710; citation_id=CR40 citation_journal_title=Arch Neurol; citation_title=Demyelinating neuropathy in diabetes mellitus; citation_author=KR Sharma, J Cross, O Farronay; citation_volume=59; citation_publication_date=2002; citation_pages=758-765; citation_doi=10.1001/archneur.59.5.758; citation_id=CR41 citation_journal_title=Muscle Nerve; citation_title=Influence of diabetes mellitus on chronic inflammatory demyelinating polyneuropathy; citation_author=KC Gorson, AH Ropper, LS Adelman, DH Weinberg; citation_volume=23; citation_publication_date=2000; citation_pages=37-43; citation_doi=10.1002/(SICI)1097-4598(200001)23:1<37::AID-MUS5>3.0.CO;2-9; citation_id=CR42 citation_journal_title=Arch Neurol; citation_title=Diabetic demyelinating polyneuropathy responsive to intravenous immunoglobulin therapy; citation_author=KR Sharma, J Cross, DR Ayyar, A Martinez-Arizala, WG Bradley; citation_volume=59; citation_publication_date=2002; citation_pages=751-757; citation_doi=10.1001/archneur.59.5.751; citation_id=CR43 citation_journal_title=Electromyogr Clin Neurophysiol; citation_title=Electrodiagnostic criteria in CIDP: comparison with diabetic neuropathy; citation_author=JR Wilson, Y Park, MR Fisher; citation_volume=40; citation_publication_date=2000; citation_pages=181-185; citation_id=CR44 citation_journal_title=Arch Neurol; citation_title=The Bruns-Garland syndrome (diabetic amyotrophy). Revisited 100 years later; citation_author=RJ Barohn, Z Sahenk, JR Warmolts, JR Mendell; citation_volume=48; citation_publication_date=1991; citation_pages=1130-1135; citation_id=CR45 citation_journal_title=Muscle Nerve; citation_title=Conduction block in diabetic neuropathy; citation_author=SR Abu-Shakra, DR Cornblath, OL Avila; citation_volume=14; citation_publication_date=1991; citation_pages=858-862; citation_doi=10.1002/mus.880140910; citation_id=CR46 citation_journal_title=Arch Neurol; citation_title=Acute renal failure resulting from intravenous immunoglobulin therapy; citation_author=E Tan, M Hajinazarian, W Bay, J Neff, JR Mendell; citation_volume=50; citation_publication_date=1993; citation_pages=137-139; citation_id=CR47 citation_journal_title=Muscle Nerve; citation_title=Proposed revised electrophysiological criteria for chronic inflammatory demyelinating polyneuropathy; citation_author=G Nicolas, T Maisonobe, N Forestier, JM Leger, P Bouche; citation_volume=25; citation_publication_date=2002; citation_pages=26-30; citation_doi=10.1002/mus.1214; citation_id=CR48