Cruveilhier-Baumgarten syndrome in which venous hum disappeared following endoscopic variceal sclerotherapy

Gastroenterologia Japonica - 1996
Osamu Yamakawa1, Hideki Ohta1, Hiroyuki Watanabe1, Yoshiharu Motoo1, Takashi Okai1, Masumi Kadoya2, Osamu Matsui2, Norio Sawabu1
1Department of Internal medicine, Cancer Research Institute, Kanazawa University, Kanazawa, Japan
2Department of Radiology, School of Medicine, Kanazawa, Japan

Tóm tắt

We report a case of Cruveihier-Baumgarten syndrome associated with portal vein thrombosis that developed, slowly during a 2-year period after, endoscopic variceal sclerotherapy. The thrombosis led to the disappearance of the venous hum and the dilated abdominal wall veins characteristic of this syndrome. A 73-year-old woman was hospitalized for treatment of esophageal varices in April 1988. Her spleen was markedly enlarged, and the histologic findings of her liver were not consistent with hepatic cirrhosis, but with idiopathic portal hypertension. A venous hum was audible in the upper abdomen. Superior mesenteric angiography revealed a porto-systemic shunt vessel under the abdominal wall, originating from the umbilical vein. She was injected four times with a sclerosant, and this brought about disappearance of the esophageal varices. Two years after the first admission, the venous hum was no longer audible, but there was a recurrence of the esophageal varices. More than 2 years later (4 years after the first admission), ultrasonographic study, computed tomography, and angiography showed a large thrombus, which completely obstructed the portal vein at the origin of the umbilical vein, and the development of collateral vessels, seen as a “cavernous transformation”.

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