Clinical characteristics and outcome of elderly onset adult-onset Still's disease: A 10-year retrospective study

Gerfaud-Valentin, 2014, Adult-onset Still's disease, Autoimmun. Rev., 13, 708, 10.1016/j.autrev.2014.01.058 Li, 2020, Autoinflammatory pathogenesis and targeted therapy for adult-onset still's disease, Clin. Rev. Allergy Immunol., 58, 71, 10.1007/s12016-019-08747-8 Yamaguchi, 1992, Preliminary criteria for classification of adult Still's disease, J. Rheumatol., 19, 424 Asanuma, 2015, Nationwide epidemiological survey of 169 patients with adult Still's disease in Japan, Mod. Rheumatol., 25, 393, 10.3109/14397595.2014.974881 Wakai, 1997, Estimated prevalence and incidence of adult Still's disease: findings by a nationwide epidemiological survey in Japan, J. Epidemiol., 7, 221, 10.2188/jea.7.221 Feist, 2018, Mechanisms, biomarkers and targets for adult-onset Still's disease, Nat. Rev. Rheumatol., 14, 603, 10.1038/s41584-018-0081-x Zhou, 2018, Biological therapy of traditional therapy-resistant adult-onset Still's disease: an evidence-based review, Therapeut. Clin. Risk Manag., 14, 167, 10.2147/TCRM.S155488 Colafrancesco, 2017, Response to interleukin-1 inhibitors in 140 Italian patients with adult-onset Still's disease: a multicentre retrospective observational study, Front. Pharmacol., 8, 369, 10.3389/fphar.2017.00369 Kaneko, 2018, Tocilizumab in patients with adult-onset still's disease refractory to glucocorticoid treatment: a randomised, double-blind, placebo-controlled phase III trial, Ann. Rheum. Dis., 77, 1720, 10.1136/annrheumdis-2018-213920 Gabay, 2018, Open-label, multicentre, dose-escalating phase II clinical trial on the safety and efficacy of tadekinig alfa (IL-18BP) in adult-onset Still's disease, Ann. Rheum. Dis., 77, 840 Bae, 2015, Reactive hemophagocytic syndrome in adult-onset Still disease: clinical features, predictive factors, and prognosis in 21 patients, Medicine (Baltim.), 94, e451, 10.1097/MD.0000000000000451 Zhang, 2016, Clinical characteristics and follow-up analysis of adult-onset Still's disease complicated by hemophagocytic lymphohistiocytosis, Clin. Rheumatol., 35, 1145, 10.1007/s10067-016-3178-0 Seo, 2017, The neutrophil-to-lymphocyte ratio could be a good diagnostic marker and predictor of relapse in patients with adult-onset Still's disease: a STROBE-compliant retrospective observational analysis, Medicine (Baltim.), 96, e7546, 10.1097/MD.0000000000007546 Takakuwa, 2019, Adult-onset Still's disease-associated interstitial lung disease represents severe phenotype of the disease with higher rate of haemophagocytic syndrome and relapse, Clin. Exp. Rheumatol., 37, 23 Gerfaud-Valentin, 2014, Adult-onset still disease: manifestations, treatment, outcome, and prognostic factors in 57 patients, Medicine (Baltim.), 93, 91, 10.1097/MD.0000000000000021 Kong, 2010, Clinical features and prognosis in adult-onset Still's disease: a study of 104 cases, Clin. Rheumatol., 29, 1015, 10.1007/s10067-010-1516-1 Ruscitti, 2016, Adult-onset Still's disease: evaluation of prognostic tools and validation of the systemic score by analysis of 100 cases from three centers, BMC Med., 14, 194, 10.1186/s12916-016-0738-8 Pouchot, 1991, Adult Still's disease: manifestations, disease course, and outcome in 62 patients, Medicine, 70, 118, 10.1097/00005792-199103000-00004 Campisi, 2019, From discoveries in ageing research to therapeutics for healthy ageing, Nature, 571, 183, 10.1038/s41586-019-1365-2 Giacomelli, 2018, A comprehensive review on adult onset Still's disease, J. Autoimmun., 93, 24, 10.1016/j.jaut.2018.07.018 Colina, 2011, The evolution of adult-onset Still disease: an observational and comparative study in a cohort of 76 Italian patients, Semin. Arthritis Rheum., 41, 279, 10.1016/j.semarthrit.2010.12.006 Kishida, 2022, Clinical characteristics and treatment of elderly onset adult-onset Still's disease, Sci. Rep., 12, 6787, 10.1038/s41598-022-10932-3 Maruyama, 2021, Clinical features of elderly-onset Adult-onset Still's disease, Mod. Rheumatol., 31, 862, 10.1080/14397595.2020.1829340 Di Cola, 2022, Adult-onset Still's disease with elderly onset: results from a multicentre study, Clin. Exp. Rheumatol., 40, 1517 Henter, 2007, HLH-2004: diagnostic and therapeutic guidelines for hemophagocytic lymphohistiocytosis, Pediatr. Blood Cancer, 48, 124, 10.1002/pbc.21039 Fardet, 2014, Development and validation of the HScore, a score for the diagnosis of reactive hemophagocytic syndrome, Arthritis Rheumatol., 66, 2613, 10.1002/art.38690 Ravelli, 2016, Ann. Rheum. Dis., 75, 481, 10.1136/annrheumdis-2015-208982 Ahn, 2017, Application of the 2016 EULAR/ACR/PRINTO classification criteria for macrophage activation syndrome in patients with adult-onset still disease, J. Rheumatol., 44, 996, 10.3899/jrheum.161286 Asakura, 2016, Proposal for new diagnostic criteria for DIC from the Japanese society on Thrombosis and Hemostasis, Thromb. J., 14, 42, 10.1186/s12959-016-0117-x Cush, 1987, Adult-onset Still's disease. Clinical course and outcome, Arthritis Rheum., 30, 186, 10.1002/art.1780300209 Masson, 1995, Adult Still's disease. Part II. Management, outcome, and prognostic factors, Rev Rhum Engl Ed, 62, 758 Pouchot, 1991, Adult Still's disease: manifestations, disease course, and outcome in 62 patients, Medicine (Baltim.), 70, 118, 10.1097/00005792-199103000-00004 Bywaters, 1971, Still's disease in the adult, Ann. Rheum. Dis., 30, 121, 10.1136/ard.30.2.121 Ohta, 1990, Adult Still's disease: a multicenter survey of Japanese patients, J. Rheumatol., 17, 1058 Gerfaud-Valentin, 2014, Adult-onset still disease: manifestations, treatment, outcome, and prognostic factors in 57 patients, Medicine (Baltim.), 93, 91, 10.1097/MD.0000000000000021 Sakata, 2016, Epidemiological study of adult-onset Still's disease using a Japanese administrative database, Rheumatol. Int., 36, 1399, 10.1007/s00296-016-3546-8 Suzuki, 2021, Clinical characteristics of Japanese patients with elderly-onset adult-onset still's disease, Tohoku J. Exp. Med., 255, 195, 10.1620/tjem.255.195 Carter, 2019, Macrophage activation syndrome in adults: recent advances in pathophysiology, diagnosis and treatment, Rheumatology, 58, 5, 10.1093/rheumatology/key006 Yang, 2019, Predictive factors and prognosis of macrophage activation syndrome associated with adult-onset Still's disease, Clin. Exp. Rheumatol., 37, 83 Gao, 2021, Clinical characteristics of macrophage activation syndrome in adult-onset Still's disease, Clin. Exp. Rheumatol., 39, 59, 10.55563/clinexprheumatol/lp2u7g Ding, 2021, Risk of macrophage activation syndrome in patients with adult-onset Still's disease with skin involvement: a retrospective cohort study, J. Am. Acad. Dermatol., 85, 1503, 10.1016/j.jaad.2021.02.005 Suda, 2020, Elderly-onset still's disease complicated by macrophage activation syndrome: a case report and review of the literature, Intern. Med., 59, 721, 10.2169/internalmedicine.3727-19 Neel, 2018, Diagnostic and management of life-threatening Adult-Onset Still Disease: a French nationwide multicenter study and systematic literature review, Crit. Care, 22, 88, 10.1186/s13054-018-2012-2 Ruscitti, 2019, Managing Adult-onset Still's disease: the effectiveness of high-dosage of corticosteroids as first-line treatment in inducing the clinical remission. Results from an observational study, Medicine (Baltim.), 98 Govoni, 2017, How I treat patients with adult onset Still's disease in clinical practice, Autoimmun. Rev., 16, 1016, 10.1016/j.autrev.2017.07.017 Franchini, 2010, Efficacy of traditional and biologic agents in different clinical phenotypes of adult-onset Still's disease, Arthritis Rheum., 62, 2530, 10.1002/art.27532