Characteristics and prospective 2-year follow-up of children with pulmonary arterial hypertension in France

Archives of Cardiovascular Diseases - Tập 103 - Trang 66-74 - 2010
Alain Fraisse1, Xavier Jais2, Jean-Marc Schleich3, Sylvie di Filippo4, Pascale Maragnès5, Maurice Beghetti6, Virginie Gressin7, Michel Voisin8, Claire Dauphin9, Pierre Clerson10, François Godart11, Damien Bonnet12
1Hôpital de la Timone, 13000 Marseille, France
2Hôpital Antoine-Béclère, 92140 Clamart, France
3Hôpital Pontchaillou, 35000 Rennes, France
4Hôpital Louis-Pradel, 69003Lyon, France
5Hôpital Côte-de-Nacre, 14000 Caen, France
6Children's Hospital, Geneva, Switzerland
7Actelion Pharmaceuticals France, 75001 Paris, France
8Hôpital Arnaud-de-Villeneuve, 34000 Montpellier, France
9Hôpital Gabriel-Montpied, 63000 Clermont-Ferrand, France
10Orgamétrie, 59100 Roubaix, France
11Hôpital cardiologique, 59000 Lille, France
12Centre de référence malformations cardiaques congénitales complexes-M3C, université Paris-Descartes, hôpital Necker–Enfants-Malades, AP–HP, 149, rue de Sèvres, 75015 Paris, France

Tài liệu tham khảo

Rubin, 1997, Primary pulmonary hypertension, N Engl J Med, 336, 111, 10.1056/NEJM199701093360207 Shafazand, 2004, Health-related quality of life in patients with pulmonary arterial hypertension, Chest, 126, 1452, 10.1378/chest.126.5.1452 D’Alonzo, 1991, Survival in patients with primary pulmonary hypertension. Results from a national prospective registry, Ann Intern Med, 115, 343, 10.7326/0003-4819-115-5-343 Humbert, 2006, Pulmonary arterial hypertension in France: results from a national registry, Am J Respir Crit Care Med, 173, 1023, 10.1164/rccm.200510-1668OC Pietra, 1989, Histopathology of primary pulmonary hypertension. A qualitative and quantitative study of pulmonary blood vessels from 58 patients in the National Heart, Lung, and Blood Institute, Primary Pulmonary Hypertension Registry, Circulation, 80, 1198, 10.1161/01.CIR.80.5.1198 Adatia, 1993, Abnormalities in the biosynthesis of thromboxane A2 and prostacyclin in children with cyanotic congenital heart disease, Br Heart J, 69, 179, 10.1136/hrt.69.2.179 Yoshibayashi, 1991, Plasma endothelin concentrations in patients with pulmonary hypertension associated with congenital heart defects. Evidence for increased production of endothelin in pulmonary circulation, Circulation, 84, 2280, 10.1161/01.CIR.84.6.2280 Rosenzweig, 2005, Idiopathic pulmonary arterial hypertension in children, Curr Opin Pediatr, 17, 372, 10.1097/01.mop.0000163356.51027.c1 Beghetti, 2006, Current treatment options in children with pulmonary arterial hypertension and experiences with oral bosentan, Eur J Clin Invest, 36, 16, 10.1111/j.1365-2362.2006.01681.x Fraisse, 2007, The French registry of pulmonary arterial hypertension in children: rational and design, Curr Med Res Opin, 23, S1, 10.1185/030079907X199501 Galie, 2004, Guidelines on diagnosis and treatment of pulmonary arterial hypertension. The Task Force on Diagnosis and Treatment of Pulmonary Arterial Hypertension of the European Society of Cardiology, Eur Heart J, 25, 2243, 10.1016/j.ehj.2004.09.014 Garofano, 1999, Exercise testing in children with primary pulmonary hypertension, Pediatr Cardiol, 20, 61, 10.1007/s002469900399 Manificat, 2000, Evaluation of the quality of life of infants and very young children: validation of a questionnaire. Multicenter European study, Arch Pediatr, 7, 605, 10.1016/S0929-693X(00)80127-X Manificat, 1997, Evaluation of the quality of life in pediatrics: how to collect the point of view of children, Arch Pediatr, 4, 1238, 10.1016/S0929-693X(97)82616-4 Ruperto, 2001, Cross-cultural adaptation and psychometric evaluation of the Childhood Health Assessment Questionnaire (CHAQ) and the Child Health Questionnaire (CHQ) in 32 countries. Review of the general methodology, Clin Exp Rheumatol, 19, S1 Landgraf, 1999 Asmussen, 2000, Use of the child health questionnaire in a sample of moderate and low-income inner-city children with asthma, Am J Respir Crit Care Med, 162, 1215, 10.1164/ajrccm.162.4.2001067 INED. Institut national d’etudes demographiques. www.ined.fr/fr/pop_chiffres/france/structure_population/sex_ages/2009. Seguchi, 2000, Pulmonary hypertension associated with pulmonary occlusive vasculopathy after allogeneic bone marrow transplantation, Transplantation, 69, 177, 10.1097/00007890-200001150-00030 Houde, 1993, Profile of paediatric patients with pulmonary hypertension judged by responsiveness to vasodilators, Br Heart J, 70, 461, 10.1136/hrt.70.5.461 Sandoval, 1995, Primary pulmonary hypertension in children: clinical characterization and survival, J Am Coll Cardiol, 25, 466, 10.1016/0735-1097(94)00391-3 Kumar, 1993, Pulmonary vascular disease in neonates with transposition of the great arteries and intact ventricular septum, Br Heart J, 69, 442, 10.1136/hrt.69.5.442 Haworth, 1983, Pulmonary hypertension in scimitar syndrome in infancy, Br Heart J, 50, 182, 10.1136/hrt.50.2.182 Rosenzweig, 2005, Effects of long-term bosentan in children with pulmonary arterial hypertension, J Am Coll Cardiol, 46, 697, 10.1016/j.jacc.2005.01.066 Barst, 1999, Vasodilator therapy for primary pulmonary hypertension in children, Circulation, 99, 1197, 10.1161/01.CIR.99.9.1197 Yung, 2004, Outcomes in children with idiopathic pulmonary arterial hypertension, Circulation, 110, 660, 10.1161/01.CIR.0000138104.83366.E9 Alonso, 2003, Functional outcomes of pediatric liver transplantation, J Pediatr Gastroenterol Nutr, 37, 155, 10.1097/00005176-200308000-00014 Humpl, 2005, Beneficial effect of oral sildenafil therapy on childhood pulmonary arterial hypertension: twelve-month clinical trial of a single-drug, open-label, pilot study, Circulation, 111, 3274, 10.1161/CIRCULATIONAHA.104.473371 Ivy, 2008, Short- and long-term effects of inhaled iloprost therapy in children with pulmonary arterial hypertension, J Am Coll Cardiol, 51, 161, 10.1016/j.jacc.2007.09.031 Haworth, 2009, Treatment and survival in children with pulmonary arterial hypertension: the UK Pulmonary Hypertension Service for Children 2001–2006, Heart, 95, 312, 10.1136/hrt.2008.150086