Abnormal pelvic morphology and high cervical length are responsible for high-risk pregnancies in women displaying achondroplasia

Orphanet Journal of Rare Diseases - Tập 11 - Trang 1-2 - 2016
Alexandre J. Vivanti1, Anne-Gael Cordier1, Geneviève Baujat2, Alexandra Benachi1
1Department of Obstetrics and Gynecology and Reproductive Medicine, AP-HP, Antoine Béclère Hospital, Univ Paris-Sud Clamart, Clamart, France
2Département de Génétique et INSERM U781, Université Paris Descartes-Sorbonne Paris Cité, Fondation Imagine, Hôpital Necker-Enfants malades, AP-HP, Paris, France

Tóm tắt

Pregnancies of women displaying achondroplasia are at high risk of adverse events. Early sonographic assessment of affected women can indicate an unusually long cervical length. It is the consequence of pathological anatomy of the pelvis. Thus, there is a foreseeable dystocia owing to cephalopelvic disproportion. Furthermore, this situation could also complicate cervical ripening prior to fetal extraction.

Tài liệu tham khảo

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