Abernethy Malformation with Liver SOL
Tóm tắt
Abernethy malformation is a very rare congenital vascular malformation with complete or partial shunting of portal flow to the systemic circulation which manifests with symptoms of recurrent respiratory tract infections and failure to thrive. We present here a case of a 12-year-old boy diagnosed as a case of Abernethy malformation.
Tài liệu tham khảo
Morgan G, Superina R (1994) Congenital absence of the portal vein: two cases and a proposed classification system for portasystemic vascular anomalies. J Pediatr Surg 29:1239–1241. https://doi.org/10.1016/0022-3468(94)90812-5
Lautz TB, Tantemsapya N, Rowell E, Superina RA (2011) Management and classification of type II congenital portosystemic shunts. J Pediatr Surg 46:308–314. https://doi.org/10.1016/j.jpedsurg.2010.11.009
Alvarez AE, Ribeiro AF, Hessel G, Baracat J, Ribeiro JD (2002) Abernethy malformation: one of the etiologies of hepatopulmonary syndrome. Pediatr Pulmonol 34:391–394. https://doi.org/10.1002/ppul.10182
Baiges A, Turon F, Simón-Talero M, Tasayco S et al (2020) Congenital extrahepatic portosystemic shunts (Abernethy malformation): an international observational study. Hepatology (Baltimore, Md.) 71:658–69. https://doi.org/10.1002/hep.30817
Zhu C, Wang M, Hao Q (2020) A case report: type II Abernethy malformation complicated with congenital polydactyly and enlargement of all cardiac chambers. Open Medicine J. 7:32–5. https://doi.org/10.2174/1874220302007010032
Kemp S (2019) Sonography aids in diagnosis of congenital absence of portal vein in patient with Marfan syndrome: a case study. J Diagnostic Medical Sonography 35:327–335. https://doi.org/10.1177/8756479319848747
Grazioli L, Alberti D, Olivetti L, Rigamonti W, Codazzi F, Matricardi L, Fugazzola C, Chiesa A (2000) Congenital absence of portal vein with nodular regenerative hyperplasia of the liver. Eur Radiol 10:820–825. https://doi.org/10.1007/s003300051012
Kumar P, Bhatia M, Garg A, Jain S, Kumar K (2022) Abernethy malformation: a comprehensive review. Diagn Interv Radiol 28:21–28. https://doi.org/10.5152/dir.2021.20474