Comparison of Common Monogenic Defects in a Large Predominantly Antibody Deficiency Cohort

The Journal of Allergy and Clinical Immunology: In Practice - Tập 7 Số 3 - Trang 864-878.e9 - 2019
Reza Yazdani1,2, Hassan Abolhassani3,1,2, Fatemeh Kiaee1,2, Sima Habibi1,2, Gholamreza Azizi4, Marzieh Tavakol4, Zahra Chavoshzadeh5, Seyed Alireza Mahdaviani6, Tooba Momen7, Mohammad Gharagozlou8, Masoud Movahedi8, Amir Ali Hamidieh9, Nasrin Behniafard10, Mohammad Nabavi11, Mohammad Hassan Bemanian11, Saba Arshi11, Rasol Molatefi12, Roya Sherkat13, Afshin Shirkani14, Reza Amin15, Soheila Aleyasin15, Reza Faridhosseini16, Farahzad Jabbari Azad16, Iraj Mohammadzadeh17, Javad Ghaffari18, Alireza Shafiei19, Arash Kalantari20, Mahboubeh Mansouri21, Mehrnaz Mesdaghi21, Delara Babaie4, Hamid Ahanchian16, Maryam Khoshkhui16, Habib Soheili22, Mohammad Hossein Eslamian23, Taher Cheraghi24, Abbas Dabbaghzadeh17, Mahmoud Tavassoli25, Rasoul Nasiri Kalmarzi26, Seyed Hamidreza Mortazavi27, Sara Kashef15, Hossein Esmaeilzadeh15, Javad Tafaroji28, Abbas Khalili29, Fariborz Zandieh19, Mahnaz Sadeghi‐Shabestari30, Sepideh Darougar5, Fatemeh Behmanesh15, Hedayat Akbari15, Mohammadreza Zandkarimi16, Farhad Abolnezhadian31, Abbas Fayezi32, Mojgan Moghtaderi15, Akefeh Ahmadiafshar32, Behzad Shakerian25, Vahid Sajedi33, Behrang Taghvaei34, Mojgan Safari23, Marzieh Heidarzadeh Arani35, Babak Ghalebaghi24, Seyed Mohammad Fathi36, Behzad Darabi37, Saeed Bazregari14, Nasrin Bazargan38, Morteza Fallahpour11, Alireza Khayatzadeh39, Naser Javahertrash11, Bahram Bashardoust5, Mohammadali Zamani40, Azam Mohsenzadeh41, Sarehsadat Ebrahimi8, Samin Sharafian8, Ahmad Vosughimotlagh8, Mitra Tafakoridelbari8, Maziar Rahim8, Parisa Ashournia8, Anahita Razaghian8, Arezou Rezaei1,2, Ashraf Samavat42, Setareh Mamishi43, Hossein Ali Khazaei44, Javad Mohammadi45, Babak Negahdari46, Nima Parvaneh1,2, Nima Rezaei1,2, Vassilios Lougaris47, Silvia Giliani48, Alessandro Plebani47, Hans D. Ochs49, Lennart Hammarström3, Asghar Aghamohammadi1,2
1Iranian Primary Immunodeficiencies Network (IPIN), Tehran University of Medical Sciences, Tehran, Iran
2Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children’s Medical Center, Tehran University of Medical Sciences, Tehran, Iran
3Division of Clinical Immunology, Department of Laboratory Medicine, Karolinska Institute at Karolinska University Hospital Huddinge, Stockholm, Sweden
4Non-Communicable Diseases Research Center, Alborz University of Medical Sciences, Karaj, Iran
5Pediatric Infections Research Center, Mofid Children’s Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran
6Pediatric Respiratory Diseases Research Center, National Research Institute of Tuberculosis and Lung Diseases (NRITLD), Shahid Beheshti University of Medical Sciences, Tehran, Iran
7Department of Allergy and Clinical Immunology, Child Growth and Development Research Center, Research Institute for Primordial Prevention of Non-Communicable Disease, Isfahan University of Medical Sciences, Isfahan, Iran;
8Division of Allergy and Clinical Immunology, Department of Pediatrics, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran
9Hematology, Oncology and Stem Cell Transplantation Research Centre, Tehran University of Medical Sciences, Tehran, Iran
10Department of Allergy and Clinical Immunology, Shahid Sadoughi University of Medical Sciences, Yazd, Iran
11Department of Allergy and Clinical Immunology, Rasool e Akram Hospital, Iran University of Medical Sciences, Tehran, Iran
12Department of Pediatrics, Bo-Ali Children's Hospital of Ardabil University of Medical Sciences, Ardabil, Iran
13Acquired Immunodeficiency Research Center, lsfahan University of Medical Sciences, Isfahan, Iran
14Allergy and Clinical Immunology Department, Bushehr University of Medical Science, School of Medicine, Bushehr, Iran
15Allergy Research Center, Shiraz University of Medical Sciences, Shiraz, Iran
16Allergy Research Center, Mashhad University of Medical Sciences, Mashhad, Iran
17Department of Allergy and Clinical Immunology, Pediatric Infectious Diseases Research Center, Faculty of Medicine, Mazandaran University of Medical Sciences, Sari, Iran
18Department of Pediatrics, Mazandaran University of Medical Sciences, Sari, Iran
19Department of Immunology, Bahrami Hospital, Tehran University of Medical Sciences, Tehran, Iran
20Department of Immunology and Allergy, Imam Khomeini Hospital, Tehran University of Medical Sciences, Tehran, Iran
21Immunology and Allergy Department, Mofid Children’s Hospital, Shahid Beheshti University of Medical Science, Tehran, Iran
22Department of Pediatrics, School of Medicine, Arak University of Medical Sciences, Arak, Iran
23Department of Pediatrics, Hamadan University of Medical Sciences, Hamadan, Iran
24Department of Pediatrics, 17th Shahrivar Children's Hospital, Guilan University of Medical Sciences, Rasht, Iran
25Department of Immunology, School of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran
26Cellular & Molecular Research Center, Kurdistan University of Medical Sciences, Sanandaj, Iran
27Department of Pediatrics, Kermanshah University of Medical Sciences, Kermanshah, Iran
28Department of Pediatrics, Qom University of Medical Sciences, Qom, Iran
29Department of Pediatrics, Shahid Sadoughi University of Medical Sciences, Yazd, Iran
30Department of Immunology and Allergy, Tabriz University of Medical Sciences, Tabriz, Iran
31Department of Immunology and Allergy, Ahvaz University of Medical Sciences, Ahvaz, Iran
32Mousavi Hospital, Zanjan University of Medical Sciences, Zanjan, Iran
33Department of Immunology and Allergy, Hormozgan University of Medical Sciences, Bandar Abbas, Iran
34Department of Immunology and Allergy, Semnan University of Medical Sciences, Semnan, Iran
35Department of Immunology and Allergy, Kashan University of Medical Sciences, Kashan, Iran
36Department of Immunology and Allergy, Qazvin University of Medical Sciences, Qazvin, Iran
37Department of Immunology and Allergy, Ilam University of Medical Sciences, Ilam, Iran
38Department of Immunology and Allergy, Kerman University of Medical Sciences, Kerman, Iran
39Department of Allergy and Clinical Immunology, Children’s Medical Center, Tehran University of Medical Sciences, Tehran, Iran
40Department of Immunology and Allergy, Shahrekord University of Medical Sciences, Shahrekord, Iran
41Department of Pediatrics, Lorestan University of Medical Sciences, Khorramabad, Iran
42Genetics Office, Centers for Disease Control and Prevention (CDC), Ministry of Health of Iran, Tehran, Iran
43Pediatric Infectious Diseases Research Center, Tehran University of Medical Sciences, Tehran, Iran
44Clinical Immunology Research Center, Zahedan University of Medical Sciences, Zahedan, Iran
45Department of Life Science, Faculty of New Science and Technology, University of Tehran, Tehran, Iran
46School of Advanced Technologies in Medicine, Department of Medical Biotechnology, Tehran University of Medical Sciences, Tehran, Iran
47Department of Experimental and Clinical Sciences, University of Brescia, Brescia, Italy
48Nocivelli Institute for Molecular Medicine and Pediatric Clinic, University of Brescia, Brescia, Italy
49Department of Pediatrics, University of Washington and Seattle Children's Research Institute, Seattle, Wash

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The Journal of Allergy and Clinical Immunology: In Practice

Tập 7 Số 3

864-878.e9

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