Calmodulin Mutants Linked to Catecholaminergic Polymorphic Ventricular Tachycardia Fail to Inhibit Human RyR2 Channels
Tóm tắt
Từ khóa
Tài liệu tham khảo
Xu, 2004, Mechanism of calmodulin inhibition of cardiac sarcoplasmic reticulum Ca2+ release channel (ryanodine receptor), Biophys J, 86, 797, 10.1016/S0006-3495(04)74155-7
Gomez-Hurtado, 2016, Novel CPVT-associated calmodulin mutation in CALM3 (CALM3-A103V) activates arrhythmogenic Ca waves and sparks, Circ Arrhythm Electrophysiol, 9, e004161, 10.1161/CIRCEP.116.004161
Hwang, 2014, Divergent regulation of ryanodine receptor 2 calcium release channels by arrhythmogenic human calmodulin missense mutants, Circ Res, 114, 1114, 10.1161/CIRCRESAHA.114.303391