Clinical features of paediatric pulmonary hypertension: a registry study

The Lancet - Tập 379 - Trang 537-546 - 2012
Rolf MF Berger1, Maurice Beghetti2, Tilman Humpl3, Gary E Raskob4, D Dunbar Ivy5, Zhi-Cheng Jing6, Damien Bonnet7, Ingram Schulze-Neick8, Robyn J Barst9
1Centre for Congenital Heart Diseases—Paediatric Cardiology, Beatrix Children's Hospital, University Medical Centre Groningen, University of Groningen, Netherlands
2Paediatric Cardiology, Children's University Hospital, Geneva, Switzerland
3Paediatric Cardiology and Critical Care Medicine, The Hospital for Sick Children University of Toronto, Toronto, ON, Canada
4College of Public Health, University of Oklahoma Health Sciences Centre, Oklahoma City, OK, USA
5Paediatrics, University of Colorado School of Medicine, Aurora, CO, USA
6Department of Cardio-Pulmonary Circulation, Shanghai Pulmonary Hospital, Tongji University School of Medicine, Shanghai, China
7Paediatric Cardiology, Université Paris Descartes, Necker Enfants Malade, Paris, France
8Great Ormond Street Hospital, London, UK
9Columbia University College of Physicians and Surgeons, New York, NY USA

Tài liệu tham khảo

Simonneau, 2009, Updated clinical classification of pulmonary hypertension, J Am Coll Cardiol, 54, S43, 10.1016/j.jacc.2009.04.012 D'Alonzo, 1991, Survival in patients with primary pulmonary hypertension. Results from a national prospective registry, Ann Intern Med, 115, 343, 10.7326/0003-4819-115-5-343 Humbert, 2006, Pulmonary arterial hypertension in France: results from a national registry, Am J Respir Crit Care Med, 173, 1023, 10.1164/rccm.200510-1668OC Frost, 2011, The changing picture of patients with pulmonary arterial hypertension in the United States: how REVEAL differs from historic and non-US contemporary registries, Chest, 139, 128, 10.1378/chest.10-0075 Galiè, 2009, Eur Heart J, 30, 2493, 10.1093/eurheartj/ehp297 McLaughlin, 2009, J Am Coll Cardiol, 53, 1573, 10.1016/j.jacc.2009.01.004 Barst, 2011, Pulmonary arterial hypertension: a comparison between children and adults, Eur Respir J, 37, 665, 10.1183/09031936.00056110 Berger, 2010, Treatment options in pediatric pulmonary arterial hypertension, Eur Respir Rev, 19, 321, 10.1183/09059180.00008410 van Loon, 2009, Clinical characterization of pediatric pulmonary hypertension: complex presentation and diagnosis, J Pediatr, 155, 176, 10.1016/j.jpeds.2009.02.036 Simonneau, 2004, Clinical classification of pulmonary hypertension, J Am Coll Cardiol, 43, S5, 10.1016/j.jacc.2004.02.037 van Loon, 2011, Pediatric pulmonary hypertension in the Netherlands: epidemiology and characterization during the period 1991 to 2005, Circulation, 124, 1755, 10.1161/CIRCULATIONAHA.110.969584 Galiè, 2006, Bosentan randomized trial of endothelin antagonist therapy-5 (BREATHE-5) investigators. Bosentan therapy in patients with Eisenmenger syndrome: a multicenter, double-blind, randomized, placebo-controlled study, Circulation, 114, 48, 10.1161/CIRCULATIONAHA.106.630715 Singh, 2006, A randomized, placebo-controlled, double-blind, crossover study to evaluate the efficacy of oral sildenafil therapy in severe pulmonary artery hypertension, Am Heart J, 151, 851.e1, 10.1016/j.ahj.2005.09.006 van Loon, 2007, Long-term effect of bosentan in adults versus children with pulmonary arterial hypertension associated with systemic-to-pulmonary shunt: does the beneficial effect persist?, Am Heart J, 154, 776, 10.1016/j.ahj.2007.06.003 Haworth, 2009, Treatment and survival in children with pulmonary arterial hypertension: the UK pulmonary hypertension service for children 2001–2006, Heart, 95, 312, 10.1136/hrt.2008.150086 Badesch, 2010, Pulmonary arterial hypertension: baseline characteristics from the REVEAL registry, Chest, 137, 376, 10.1378/chest.09-1140 Stenmark, 2005, Lung vascular development: implications for the pathogenesis of bronchopulmonary dysplasia, Annu Rev Physiol, 67, 623, 10.1146/annurev.physiol.67.040403.102229 Khemani, 2007, Pulmonary artery hypertension in formerly premature infants with bronchopulmonary dysplasia: clinical features and outcomes in the surfactant era, Pediatrics, 120, 1260, 10.1542/peds.2007-0971 Jobe, 2011, The new bronchopulmonary dysplasia, Curr Opin Pediatr, 23, 167, 10.1097/MOP.0b013e3283423e6b Kessler, 2001, Natural history of pulmonary hypertension in a series of 131 patients with chronic obstructive pulmonary disease, Am J Respir Crit Care Med, 164, 219, 10.1164/ajrccm.164.2.2006129 Chi, 1975, The pulmonary vascular bed in children with Down syndrome, J Pediatr, 86, 533, 10.1016/S0022-3476(75)80142-9 McDowell, 2011, Pulmonary complications of Down syndrome during childhood, J Pediatr, 158, 319, 10.1016/j.jpeds.2010.07.023 Marcus, 1991, Obstructive sleep apnea in children with Down syndrome, Pediatrics, 88, 132, 10.1542/peds.88.1.132 Cooney, 1982, Pulmonary hypoplasia in Down syndrome, N Engl J Med, 307, 1170, 10.1056/NEJM198211043071902 Pfizer Le, 2011, Syncope in adults with pulmonary arterial hypertension, J Am Coll Cardiol, 58, 863, 10.1016/j.jacc.2011.04.026 Rosenzweig, 2008, Pulmonary arterial hypertension in children: a medical update, Curr Opin Pediatr, 20, 288, 10.1097/MOP.0b013e3282ff5fdc