FHR5 Binds to Laminins, Uses Separate C3b and Surface-Binding Sites, and Activates Complement on Malondialdehyde-Acetaldehyde Surfaces

Journal of Immunology - Tập 200 Số 7 - Trang 2280-2290 - 2018
Ramona B. Rudnick1, Qian Chen1, Emma Diletta Stea1, Andrea Hartmann1, Nikolina Papac-Miličević2,3, Fermín Person4, Michael S. Wiesener5, Christoph J. Binder2,3, Thorsten Wiech4, Christine Skerka1, Peter F. Zipfel1,6
1*Department of Infection Biology, Leibniz Institute for Natural Product Research and Infection Biology, 07745 Jena, Germany;
2†Clinical Department of Medical and Chemical Laboratory Diagnostics, Medical University of Vienna, 1090 Vienna, Austria;
3Research Center for Molecular Medicine of the Austrian Academy of Sciences, 1090 Vienna, Austria
4§Institute of Pathology, University Hospital Hamburg-Eppendorf, 20246 Hamburg, Germany;
5¶Department of Nephrology and Hypertension, Friedrich-Alexander University of Erlangen-Nuremberg, 91054 Erlangen, Germany; and
6‖Department Microbiology, Friedrich-Schiller-University, 07745 Jena, Germany

Tóm tắt

Abstract

Factor H related-protein 5 (CFHR5) is a surface-acting complement activator and variations in the CFHR5 gene are linked to CFHR glomerulonephritis. In this study, we show that FHR5 binds to laminin-521, the major constituent of the glomerular basement membrane, and to mesangial laminin-211. Furthermore, we identify malondialdehyde-acetaldehyde (MAA) epitopes, which are exposed on the surface of human necrotic cells (Homo sapiens), as new FHR5 ligands. Using a set of novel deletion fragments, we show that FHR5 binds to laminin-521, MAA epitopes, heparin, and human necrotic cells (HUVECs) via the middle region [short consensus repeats (SCRs) 5-7]. In contrast, surface-bound FHR5 contacts C3b via the C-terminal region (SCRs8-9). Thus, FHR5 uses separate domains for C3b binding and cell surface interaction. MAA epitopes serve as a complement-activating surface by recruiting FHR5. The complement activator FHR5 and the complement inhibitor factor H both bind to oxidation-specific MAA epitopes and FHR5 competes with factor H for binding. The C3 glomerulopathy–associated FHR21–2-FHR5 hybrid protein is more potent in MAA epitope binding and activation compared with wild-type FHR5. The implications of these results for pathology of CFHR glomerulonephritis are discussed. In conclusion, we identify laminins and oxidation-specific MAA epitopes as novel FHR5 ligands and show that the surface-binding site of FHR5 (SCRs5-7) is separated from the C3b binding site (SCRs8-9). Furthermore, FHR5 competes with factor H for binding to MAA epitopes and activates complement on these modified structures.

Từ khóa


Tài liệu tham khảo

Zipfel, 2009, Complement regulators and inhibitory proteins., Nat. Rev. Immunol., 9, 729, 10.1038/nri2620

Sarma, 2011, The complement system., Cell Tissue Res., 343, 227, 10.1007/s00441-010-1034-0

Mathern, 2015, Molecules great and small: the complement system., Clin. J. Am. Soc. Nephrol., 10, 1636, 10.2215/CJN.06230614

Józsi, 2008, Factor H family proteins and human diseases., Trends Immunol., 29, 380, 10.1016/j.it.2008.04.008

Skerka, 2013, Complement factor H related proteins (CFHRs)., Mol. Immunol., 56, 170, 10.1016/j.molimm.2013.06.001

McRae, 2005, Human factor H-related protein 5 has cofactor activity, inhibits C3 convertase activity, binds heparin and C-reactive protein, and associates with lipoprotein., J. Immunol., 174, 6250, 10.4049/jimmunol.174.10.6250

Chen, 2016, Complement factor H-related 5-hybrid proteins anchor properdin and activate complement at self-surfaces., J. Am. Soc. Nephrol., 27, 1413, 10.1681/ASN.2015020212

Csincsi, 2015, Factor H-related protein 5 interacts with pentraxin 3 and the extracellular matrix and modulates complement activation., J. Immunol., 194, 4963, 10.4049/jimmunol.1403121

Goicoechea de Jorge, 2013, Dimerization of complement factor H-related proteins modulates complement activation in vivo., Proc. Natl. Acad. Sci. USA, 110, 4685, 10.1073/pnas.1219260110

Kopp, 2012, Factor H: a complement regulator in health and disease, and a mediator of cellular interactions., Biomolecules, 2, 46, 10.3390/biom2010046

Oppermann, 2006, The C-terminus of complement regulator Factor H mediates target recognition: evidence for a compact conformation of the native protein., Clin. Exp. Immunol., 144, 342, 10.1111/j.1365-2249.2006.03071.x

Gordon, 1995, Identification of complement regulatory domains in human factor H., J. Immunol., 155, 348, 10.4049/jimmunol.155.1.348

Kühn, 1996, Mapping of the domains required for decay acceleration activity of the human factor H-like protein 1 and factor H., Eur. J. Immunol., 26, 2383, 10.1002/eji.1830261017

Manuelian, 2003, Mutations in factor H reduce binding affinity to C3b and heparin and surface attachment to endothelial cells in hemolytic uremic syndrome., J. Clin. Invest., 111, 1181, 10.1172/JCI16651

Sharma, 1996, Identification of three physically and functionally distinct binding sites for C3b in human complement factor H by deletion mutagenesis., Proc. Natl. Acad. Sci. USA, 93, 10996, 10.1073/pnas.93.20.10996

Jokiranta, 2005, Binding of complement factor H to endothelial cells is mediated by the carboxy-terminal glycosaminoglycan binding site., Am. J. Pathol., 167, 1173, 10.1016/S0002-9440(10)61205-9

Gale, 2010, Identification of a mutation in complement factor H-related protein 5 in patients of Cypriot origin with glomerulonephritis., Lancet, 376, 794, 10.1016/S0140-6736(10)60670-8

Servais, 2007, Primary glomerulonephritis with isolated C3 deposits: a new entity which shares common genetic risk factors with haemolytic uraemic syndrome., J. Med. Genet., 44, 193, 10.1136/jmg.2006.045328

Hageman, 2005, A common haplotype in the complement regulatory gene factor H (HF1/CFH) predisposes individuals to age-related macular degeneration., Proc. Natl. Acad. Sci. USA, 102, 7227, 10.1073/pnas.0501536102

Edwards, 2005, Complement factor H polymorphism and age-related macular degeneration., Science, 308, 421, 10.1126/science.1110189

Zhang, 2012, Causes of alternative pathway dysregulation in dense deposit disease., Clin. J. Am. Soc. Nephrol., 7, 265, 10.2215/CJN.07900811

Gale, 2011, Regulating complement in the kidney: insights from CFHR5 nephropathy., Dis. Model. Mech., 4, 721, 10.1242/dmm.008052

Zipfel, 2007, Deletion of complement factor H-related genes CFHR1 and CFHR3 is associated with atypical hemolytic uremic syndrome., PLoS Genet., 3, e41, 10.1371/journal.pgen.0030041

Chen, 2014, Complement factor H-related hybrid protein deregulates complement in dense deposit disease., J. Clin. Invest., 124, 145, 10.1172/JCI71866

Abrera-Abeleda, 2006, Variations in the complement regulatory genes factor H (CFH) and factor H related 5 (CFHR5) are associated with membranoproliferative glomerulonephritis type II (dense deposit disease)., J. Med. Genet., 43, 582, 10.1136/jmg.2005.038315

Zhai, 2016, Rare variants in the complement factor H-related protein 5 gene contribute to genetic susceptibility to IgA nephropathy., J. Am. Soc. Nephrol., 27, 2894, 10.1681/ASN.2015010012

Westra, 2012, Atypical hemolytic uremic syndrome and genetic aberrations in the complement factor H-related 5 gene., J. Hum. Genet., 57, 459, 10.1038/jhg.2012.57

Togarsimalemath, 2017, A novel CFHR1-CFHR5 hybrid leads to a familial dominant C3 glomerulopathy., Kidney Int., 92, 876, 10.1016/j.kint.2017.04.025

Xiao, 2016, Familial C3 glomerulonephritis caused by a novel CFHR5-CFHR2 fusion gene., Mol. Immunol., 77, 89, 10.1016/j.molimm.2016.07.007

Medjeral-Thomas, 2014, A novel CFHR5 fusion protein causes C3 glomerulopathy in a family without Cypriot ancestry., Kidney Int., 85, 933, 10.1038/ki.2013.348

Weismann, 2011, Complement factor H binds malondialdehyde epitopes and protects from oxidative stress., Nature, 478, 76, 10.1038/nature10449

Veneskoski, 2011, Specific recognition of malondialdehyde and malondialdehyde acetaldehyde adducts on oxidized LDL and apoptotic cells by complement anaphylatoxin C3a., Free Radic. Biol. Med., 51, 834, 10.1016/j.freeradbiomed.2011.05.029

Binder, 2016, Innate sensing of oxidation-specific epitopes in health and disease., Nat. Rev. Immunol., 16, 485, 10.1038/nri.2016.63

Miller, 2011, Oxidation-specific epitopes are danger-associated molecular patterns recognized by pattern recognition receptors of innate immunity., Circ. Res., 108, 235, 10.1161/CIRCRESAHA.110.223875

Chang, 2004, Apoptotic cells with oxidation-specific epitopes are immunogenic and proinflammatory., J. Exp. Med., 200, 1359, 10.1084/jem.20031763

Tsiantoulas, 2015, Circulating microparticles carry oxidation-specific epitopes and are recognized by natural IgM antibodies., J. Lipid Res., 56, 440, 10.1194/jlr.P054569

Weismann, 2012, The innate immune response to products of phospholipid peroxidation., Biochim. Biophys. Acta, 1818, 2465, 10.1016/j.bbamem.2012.01.018

Esterbauer, 1991, Chemistry and biochemistry of 4-hydroxynonenal, malonaldehyde and related aldehydes., Free Radic. Biol. Med., 11, 81, 10.1016/0891-5849(91)90192-6

Tuma, 2002, Role of malondialdehyde-acetaldehyde adducts in liver injury., Free Radic. Biol. Med., 32, 303, 10.1016/S0891-5849(01)00742-0

Eberhardt, 2013, Human factor H-related protein 2 (CFHR2) regulates complement activation., PLoS One, 8, e78617, 10.1371/journal.pone.0078617

Chou, 2009, Oxidation-specific epitopes are dominant targets of innate natural antibodies in mice and humans., J. Clin. Invest., 119, 1335, 10.1172/JCI36800

Xu, 1997, Epitope characterization of malondialdehyde-acetaldehyde adducts using an enzyme-linked immunosorbent assay., Chem. Res. Toxicol., 10, 978, 10.1021/tx970069t

Amir, 2012, Peptide mimotopes of malondialdehyde epitopes for clinical applications in cardiovascular disease., J. Lipid Res., 53, 1316, 10.1194/jlr.M025445

Schindelin, 2012, Fiji: an open-source platform for biological-image analysis., Nat. Methods, 9, 676, 10.1038/nmeth.2019

Buhlmann, 2016, FHR3 blocks C3d-mediated coactivation of human B cells., J. Immunol., 197, 620, 10.4049/jimmunol.1600053

Setty, 2012, Differential expression of laminin isoforms in diabetic nephropathy and other renal diseases., Mod. Pathol., 25, 859, 10.1038/modpathol.2011.216

Miner, 2012, The glomerular basement membrane., Exp. Cell Res., 318, 973, 10.1016/j.yexcr.2012.02.031

Lauer, 2011, Complement regulation at necrotic cell lesions is impaired by the age-related macular degeneration-associated factor-H His402 risk variant., J. Immunol., 187, 4374, 10.4049/jimmunol.1002488

Zipfel, 1999, FHL-1/reconectin: a human complement and immune regulator with cell-adhesive function., Immunol. Today, 20, 135, 10.1016/S0167-5699(98)01432-7

Murphy, 2002, Factor H-related protein-5: a novel component of human glomerular immune deposits., Am. J. Kidney Dis., 39, 24, 10.1053/ajkd.2002.29873

Sethi, 2009, Glomeruli of dense deposit disease contain components of the alternative and terminal complement pathway., Kidney Int., 75, 952, 10.1038/ki.2008.657

Dunér, 2010, Immune responses against aldehyde-modified laminin accelerate atherosclerosis in Apoe-/- mice., Atherosclerosis, 212, 457, 10.1016/j.atherosclerosis.2010.07.014

Tortajada, 2017, Elevated factor H-related protein 1 and factor H pathogenic variants decrease complement regulation in IgA nephropathy., Kidney Int., 92, 953, 10.1016/j.kint.2017.03.041