Validation of a predictive survival model in Italian patients with cystic fibrosis

Kerem, 1992, Prediction of mortality in patients with cystic fibrosis, N Engl J Med, 326, 1187, 10.1056/NEJM199204303261804

Liou, 2001, Predictive 5-year survivorship model of cystic fibrosis, Am J Epidemiol, 153, 345, 10.1093/aje/153.4.345

Aigner, 2004, Cystic fibrosis and lung transplantation—determination of the survival benefit, Wien Klin Wochenschr, 116, 318, 10.1007/BF03040902

Augarten, 2001, Prediction of mortality and timing of referral for lung transplantation in cystic fibrosis patients, Pediatr Transplant, 5, 339, 10.1034/j.1399-3046.2001.00019.x

Hofer, 2009, True survival benefit of lung transplantation for cystic fibrosis patients: the Zurich experience, J Heart Lung Transplant, 28, 334, 10.1016/j.healun.2008.12.025

Efrati, 2006, Long term nutritional rehabilitation by gastrostomy in Israeli patients with cystic fibrosis: clinical outcome in advanced pulmonary disease, J Pediatr Gastroenterol Nutr, 42, 222, 10.1097/01.mpg.0000189348.09925.02

Hankinson, 1999, Spirometric reference values from a sample of the general US population, Am J Respir Crit Care Med, 159, 179, 10.1164/ajrccm.159.1.9712108

Lai, 1998, Growth status in children with cystic fibrosis based on the National Cystic Fibrosis Patient Registry data: evaluation of various criteria used to identify malnutrition, J Pediatr, 132, 478, 10.1016/S0022-3476(98)70024-1

Dibley, 1987, Development of normalized curves for the international growth reference: historical and technical considerations, Am J Clin Nutr, 46, 736, 10.1093/ajcn/46.5.736

Viviani, 2003, The Italian registry for cystic fibrosis: what has changed in the last decade, Epidemiol Prev, 27, 91

Liou, 2005, Use of lung transplantation survival models to refine patient selection in cystic fibrosis, Am J Respir Crit Care Med, 171, 1053, 10.1164/rccm.200407-900OC

Lucidi, 2009, Growth assessment of paediatric patients with CF comparing different auxologic indicators: a multicentre Italian study, J Pediatr Gastroenterol Nutr, 49, 335, 10.1097/MPG.0b013e31818f0a39

Bossi, 2004, Assemblea Dei Direttori Dei Centri. What is the incidence of cystic fibrosis in Italy? Data from the National Registry (1988–2001), Hum Biol, 76, 455, 10.1353/hub.2004.0040

Corey, 1996, Determinants of mortality from cystic fibrosis in Canada, 1970–1989, Am J Epidemiol, 143, 1007, 10.1093/oxfordjournals.aje.a008664

George, 2011, Improved survival at low lung function in cystic fibrosis: cohort study from 1990 to 2007, BMJ, 342, d1008, 10.1136/bmj.d1008

Dodge, 2007, Cystic fibrosis mortality and survival in the UK: 1947–2003, Eur Respir J, 29, 522, 10.1183/09031936.00099506

McKone, 2003, Effect of genotype on phenotype and mortality in cystic fibrosis: a retrospective cohort study, Lancet, 361, 1671, 10.1016/S0140-6736(03)13368-5

Buzzetti, 2009, An overview of international literature from cystic fibrosis registries: 1. Mortality and survival studies in cystic fibrosis, J Cyst Fibros, 8, 229, 10.1016/j.jcf.2009.04.001

Jackson, 2011, The application of current lifetable methods to compare cystic fibrosis median survival internationally is limited, J Cyst Fibros, 10, 62, 10.1016/j.jcf.2010.08.021

Cystic Fibrosis Foundation, 2008

McCormick, 2010, Comparative demographics of the European cystic fibrosis population: a cross-sectional database analysis, Lancet, 375, 1007, 10.1016/S0140-6736(09)62161-9

Davis, 2006, Cystic fibrosis since 1938, Am J Respir Crit Care Med, 173, 475, 10.1164/rccm.200505-840OE

Grasemann, 2010, Emerging therapies for cystic fibrosis lung disease, Expert Opin Emerg Drugs, 15, 653, 10.1517/14728214.2010.517746

Heijerman, 2009, Inhaled medication and inhalation devices for lung disease in patients with cystic fibrosis: a European consensus, J Cyst Fibros, 8, 295, 10.1016/j.jcf.2009.04.005

Moran, 2009, Non-invasive ventilation for cystic fibrosis, Cochrane Database Syst Rev, 1, CD002769

Dodge, 2005, Cystic fibrosis is no longer an important cause of childhood death in the UK, Arch Dis Child, 90, 547

Kulich, 2003, Improved survival among young patients with cystic fibrosis, J Pediatr, 142, 631, 10.1067/mpd.2003.197

Finkelstein, 1988, Diabetes mellitus associated with cystic fibrosis, J Pediatr, 112, 373, 10.1016/S0022-3476(88)80315-9

Moran, 2009, Cystic fibrosis-related diabetes: current trends in prevalence, incidence, and mortality, Diabetes Care, 32, 1626, 10.2337/dc09-0586

Chamnan, 2010, Diabetes as a determinant of mortality in cystic fibrosis, Diabetes Care, 33, 311, 10.2337/dc09-1215

Mayer-Hamblett, 2002, Developing cystic fibrosis lung transplant referral criteria using predictors of 2-year mortality, Am J Respir Crit Care Med, 166, 1550, 10.1164/rccm.200202-087OC

Li, 2005, Longitudinal development of mucoid Pseudomonas aeruginosa infection and lung disease progression in children with cystic fibrosis, JAMA, 293, 581, 10.1001/jama.293.5.581

Demko, 1995, Gender differences in cystic fibrosis: Pseudomonas aeruginosa infection, J Clin Epidemiol, 48, 1041, 10.1016/0895-4356(94)00230-N

Levy, 2008, Predictors of mucoid Pseudomonas colonization in cystic fibrosis patients, Pediatr Pulmonol, 43, 463, 10.1002/ppul.20794

Goss, 2011, Review: Staphylococcus aureus and MRSA in cystic fibrosis, J Cyst Fibros, 10.1016/j.jcf.2011.06.002