N-terminal Domains of Human Copper-transporting Adenosine Triphosphatases (the Wilson's and Menkes Disease Proteins) Bind Copper Selectively in Vivo and in Vitro with Stoichiometry of One Copper Per Metal-binding Repeat

Journal of Biological Chemistry - Tập 272 Số 30 - Trang 18939-18944 - 1997
Svetlana Lutsenko1, Konstantin Petrukhin2, Matthew J. Cooper1, Conrad Gilliam3, Jack H. Kaplan1
1Department of Biochemistry and Molecular Biology, Oregon Health Sciences University, Portland, Oregon 97201
2Department of Human Genetics, Merck Research Laboratories, West Point, Pennsylvania, 19486
3Departments of Genetics, Development, and Psychiatry at Columbia University and New York State Psychiatric Institute, New York, New York 10032

Tóm tắt

Từ khóa


Tài liệu tham khảo

Danks, 1989, 1411

Vulpe, 1995, Annu. Rev. Nutr., 15, 293, 10.1146/annurev.nu.15.070195.001453

Tomas, 1995, Nat. Genet., 9, 210, 10.1038/ng0295-210

Vulpe, 1993, Nat. Genet., 3, 7, 10.1038/ng0193-7

Tanzi, 1993, Nat. Genet., 5, 344, 10.1038/ng1293-344

Bull, 1993, Nat. Genet., 5, 327, 10.1038/ng1293-327

Kaler, 1994, Nat. Genet., 8, 195, 10.1038/ng1094-195

Petrukhin, 1994, Hum. Mol. Genet., 3, 1647, 10.1093/hmg/3.9.1647

Yamaguchi, 1993, Biochem. Biophys. Res. Commun., 197, 271, 10.1006/bbrc.1993.2471

Lutsenko, 1995, Biochemistry, 34, 15607, 10.1021/bi00048a001

Nucifora, 1989, Proc. Natl. Acad. Sci. USA, 86, 3544, 10.1073/pnas.86.10.3544

Walsh, 1988, FASEB J., 2, 124, 10.1096/fasebj.2.2.3277886

Silver, 1993, Mol. Microbiol., 10, 7, 10.1111/j.1365-2958.1993.tb00898.x

Solioz, 1994, FEBS Lett., 346, 44, 10.1016/0014-5793(94)00316-5

Lappalainen, 1993, J. Biol. Chem., 268, 26416, 10.1016/S0021-9258(19)74330-0

Harris, 1986, Mol. Biol. Med., 3, 279

Bradford, 1976, Anal. Biochem., 72, 248, 10.1016/0003-2697(76)90527-3

Laemmli, 1970, Nature, 227, 680, 10.1038/227680a0

Brenner, 1995, Anal. Biochem., 226, 80, 10.1006/abio.1995.1194

Yasukawa, 1995, J. Biol. Chem., 270, 25328, 10.1074/jbc.270.43.25328

Speno, 1995, J. Biol. Chem., 270, 25363, 10.1074/jbc.270.43.25363

Lutsenko, S., Petrukhin, K., Gilliam, T. C., and Kaplan, J. H. (1997)Annu. Rev. Acad. Sci., N. Y. in press.