Three cases of pneumatosis intestinalis presenting in autoimmune diseases

Oxford University Press (OUP) - Tập 22 - Trang 610-615 - 2011
Akihiro Sagara1,2, Kiyoki Kitagawa2, Kengo Furuichi2, Shinji Kitajima2, Tadashi Toyama2, Toshiya Okumura1,2, Akinori Hara2, Yoshio Sakai3, Shuichi Kaneko2, Takashi Wada3
1Department of Nephrology and Hypertension, Tonami General Hospital, Tonami, Japan
2Department of Disease Control and Homeostasis, Institute of Medical, Pharmaceutical and Health Sciences, Faculty of Medicine, Kanazawa University, Kanazawa, Japan
3Department of Laboratory Medicine, Institute of Medical, Pharmaceutical and Health Sciences, Faculty of Medicine, Kanazawa University, Kanazawa, Japan

Tóm tắt

Pneumatosis intestinalis (PI) is a comparatively rare disease characterized by the presence of intramural gas in the gastrointestinal tract. PI is known to be associated with several clinical conditions, such as pulmonary diseases, gastrointestinal diseases, and traumatic injury, as well as autoimmune disorders. In particular, PI is commonly seen in systemic sclerosis (SSc) but rarely in systemic lupus erythematosus and dermatomyositis (DM). In this report, we present three cases of PI presenting in autoimmune diseases, including DM, Sjögren’s syndrome, and limited SSc, and further discuss its background characteristics.

Tài liệu tham khảo

Heng Y, Schuffler MD, Haggitt RC, Rohrmann CA. Pneumatosis intestinalis: a review. Am J Gastroenterol. 1995;90:1747–58. Sequeira W. Pneumatosis cystoides intestinalis in systemic sclerosis and other diseases. Semin Arthritis Rheum. 1990;19:269–77. Jamart J. Pneumatosis cystoids intestinalis. A statistical study of 919 cases. Acta Hepatogastroenterol. 1979;26:419–22. Ebert EC. Gastric and enteric involvement in progressive systemic sclerosis. J Clin Gastroenterol. 2008;42:5–12. Cabrera GE, Scopelitis E, Cuellar ML, Silveira LH, Mena H, Espinozal LR. Pneumatosis cystoids intestinalis in systemic lupus erythematosus with intestinal vasculitis: treatment with high dose prednisone. Clin Rheumatol. 1994;13:312–6. Mizoguchi F, Nanki T, Miyasaka N. Pneumatosis cystoides intestinalis following lupus enteritis and peritonitis. Intern Med. 2008;47:1267–71. Pasquier E, Wattiaux MJ, Peigney N. First case of pneumatosis cystoides intestinalis in adult dermatomyositis. J Rheumatol. 1993;20:499–503. Morris-Stiff GJ, Williams RJ. Pneumatosis cystoides intestinalis in a patient with dermatomyositis. J R Soc Med. 1999;92:366–7. Xiao T, Xu HH, Wu J, He CD, Chen HD. Case of pneumatosis cystoides intestinalis in adult dermatomyositis. J Dermatol. 2008;35:49–51. St Peter SD, Abbas MA, Kelly KA. The spectrum of pneumatosis intestinalis. Arch Surg. 2003;138:68–75. Yale CE, Balish E, Wu JP. The bacterial etiology of pneumatosis cystoids intestinalis. Arch Surg. 1974;109:89–94. Florin TH. Alkyl halides, super hydrogen production and the pathogenesis of pneumatosis cystoides coli. Gut. 1997;41:778–84. Fenton LZ, Buonomo C. Benign pneumatosis in children. Pediatr Radiol. 2000;30:786–93. Ammons MA, Bauling PC, Weil R 3rd. Pneumatosis cystoides intestinalis with pneumoperitoneum in renal transplant patients on cyclosporine and prednisone. Transpl Proc. 1986;18:1868–70. Morris MS, Gee AC, Cho SD, Limbaugh K, Underwood S, Ham B, Schreiber MA. Management and outcome of pneumatosis intestinalis. Am J Surg. 2008;195:679–82. Ho LM, Paulson EK, Thompson WM. Pneumatosis intestinalis in the adult: benign to life-threatening causes. Am J Roentgenol. 2007;188:1604–13. Ellis BW. Symptomatic treatment of primary pneumatosis coli with metronidazole. Br Med J. 1980;15:763–4. Holt S, Gilmour HM, Buist TA, Marwick K, Heading RC. High flow oxygen therapy for pneumatosis coli. Gut. 1979;20:493–8. Grieve DA, Unsworth IP. Pneumatosis cystoides intestinalis: an experience with hyperbaric oxygen treatment. Aust N Z J Surg. 1991;61:423–6. Greenstein AJ, Nguyen SQ, Berlin A, Corona J, Lee J, Wong E, Factor SH, Divino CM. Pneumatosis intestinalis in adults: management, surgical indications, and risk factors for mortality. J Gastrointest Surg. 2007;11:1268–74. Wayne E, Ough M, Wu A, Liao J, Andresen KJ, Kuehn D, Wilkinson N. Management algorithm for pneumatosis intestinalis and portal venous gas: treatment and outcome of 88 consecutive cases. J Gastrointest Surg. 2010;14:437–48.