PMP22-related disease: A novel splice site acceptor variant and intrafamilial phenotype variability

Neuromuscular Disorders - Tập 29 - Trang 422-426 - 2019
Toshitaka Kawarai1, Hiroki Yamazaki1, Ryosuke Miyamoto1, Naoko Takamatsu1, Atsuko Mori1, Yusuke Osaki1, Antonio Orlacchio2,3, Hiroyuki Nodera1, Akihiro Hashiguchi4, Yujiro Higuchi4, Akiko Yoshimura4, Hiroshi Takashima4, Ryuji Kaji1
1Department of Clinical Neuroscience, Tokushima University Graduate School, Tokushima, Japan
2Laboratorio di Neurogenetica, Centro Europeo di Ricerca sul Cervello (CERC) - Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) Fondazione Santa Lucia, Rome, Italy
3Dipartimento di Scienze Chirurgiche e Biomediche, Università di Perugia, Perugia, Italy
4Department of Neurology and Geriatrics, Kagoshima University Graduate School of Medical and Dental Sciences, Kagoshima, Japan

Tài liệu tham khảo

Gutmann, 2015, Update on Charcot–Marie–Tooth disease, Curr Opin Neurol, 28, 462, 10.1097/WCO.0000000000000237 Nodera, 2003, HNPP due to a novel missense mutation of the PMP22 gene, Neurology, 60, 1863, 10.1212/01.WNL.0000066049.13848.F2 Passage, 2004, Ascorbic acid treatment corrects the phenotype of a mouse model of Charcot–Marie–Tooth disease, Nat Med, 10, 396, 10.1038/nm1023 Meyer zu Horste, 2007, Antiprogesterone therapy uncouples axonal loss from demyelination in a transgenic rat model of CMT1A neuropathy, Ann Neurol, 61, 61, 10.1002/ana.21026 Kawarai, 2016, MFN2 transcripts escaping from nonsense-mediated mRNA decay pathway cause Charcot–Marie–Tooth disease type 2A2, J Neurol Neurosurg Psychiatry, 87, 1263, 10.1136/jnnp-2015-312646 Bird, 1993, Hereditary neuropathy with liability to pressure palsies Leblhuber, 1991, Clinical and electrodiagnostic findings, nerve biopsy and blood group markers in a family with hereditary neuropathy with liability to pressure palsies, Acta Neurol Scand, 83, 166, 10.1111/j.1600-0404.1991.tb04670.x Wang, 2017, PMP22 exon 4 deletion causes ER retention of PMP22 and a gain-of-function allele in CMT1E, Ann Clin Transl Neurol, 4, 236, 10.1002/acn3.395