Park, 1981, Gastrointestinal manifestions of cystic fibrosis: A review, Gastroenterology, 81, 1143, 10.1016/S0016-5085(81)80027-3
Donnison, 1966, A review of 164 children with meconium ileus seen at the Children's Hospital Medical Center, Boston, Pediatrics, 37, 833, 10.1542/peds.37.5.833
Antonowicz, 1979, Meconium in health and disease, Adv. Pediatr., 26, 275, 10.1016/S0065-3101(22)00677-6
Oppenheimer, 1973, Cystic fibrosis of the pancreas, morphologic findings in infants with and without pancreatic lesions, Arch. Pathol., 96, 149
Leonidas, 1970, Meconium ileus and its complications: A reappraisal of plain film roentgen diagnostic criteria, A.J.R., 108, 598
White, 1956, Meconium ileus: A new roentgen sign, Radiology, 66, 567, 10.1148/66.4.567
Rickham, 1965, Neonatal meconium obstruction in the absence of mucoviscidosis, Am. J. Surg., 109, 173
Hiatt, 1948, Coeliac syndrome: VII. Therapy of meconium ileus, report of eight cases with a review of the literature, Surg. Gynecol. Obstet., 87, 317
McPartlin, 1972, Meconium ileus: Immediate and long-term survival, Arch. Dis. Child., 47, 207, 10.1136/adc.47.252.207
Rowe, 1973, Gastrografin-induced hypertonicity: The pathogenesis of a neonatal hazard, Am. J. Surg., 125, 185, 10.1016/0002-9610(73)90025-1
Gaskin, 1982, Improved respiratory prognosis in patients with cystic fibrosis with normal fat absorption, J. Pediatr., 100, 857, 10.1016/S0022-3476(82)80501-5
Imrie, 1979, Quantitative evaluation of the development of the exocrine pancreas in cystic fibrosis and control infants, Am. J. Pathol., 95, 697
Shmerling, 1970, Fecal fat and nitrogen in healthy children, and in children with malabsorption or maldigestion, Pediatrics, 46, 690, 10.1542/peds.46.5.690
Gaskin, 1984, Colipase and lipase secretion in childhood onset pancreatic insufficiency, Gastroenterology, 86, 1, 10.1016/0016-5085(84)90582-1
Abrams, 1984, Lingual lipase in cystic fibrosis: Quantitation of enzyme activity in the upper and small intestine of patients with exocrine pancreatic insufficiency, J. Clin. Invest., 73, 374, 10.1172/JCI111222
Roulet, 1980, Increased gastric lipolytic activity in cystic fibrosis, 173
Nielsen, 1982, The incidence of anemia, hypoproteinemia and edema in infants as presenting symptoms of cystic fibrosis: A retrospective survey of the frequency of this symptom complex in 130 patients with cystic fibrosis, J. Pediatr. Gastroenterol. Nutr., 1, 355, 10.1097/00005176-198201030-00013
Fleisher, 1964, Hypoproteinemia and edema in infants with cystic fibrosis of the pancreas, J. Pediatr., 64, 341, 10.1016/S0022-3476(64)80186-4
Strober, 1969, Albumin metabolism in cystic fibrosis, Pediatrics, 43, 416, 10.1542/peds.43.3.416
Kulczycki, 1958, Studies in cystic fibrosis of the pancreas: Occurrence of rectal prolapse, N. Engl. J. Med., 259, 409, 10.1056/NEJM195808282590901
Stern, 1982, Treatment and prognosis of rectal prolapse in cystic fibrosis, Gastroenterology, 82, 707, 10.1016/0016-5085(82)90315-8
Gurwitz, 1979, Perspectives in cystic fibrosis, Pediatr. Clin. North Am., 26, 603, 10.1016/S0031-3955(16)33752-X
Cox, 1980, Gastric acid hypersecretion in cystic fibrosis, abstracted, Clin. Res., 28, 96
Weber, 1973, Malabsorption of bile acids in children with cystic fibrosis, N. Engl. J. Med., 289, 1001, 10.1056/NEJM197311082891903
Boyle, 1980, Effect of cimetidine and pancreatic enzymes on serum and fecal bile acids and fat absorption in cystic fibrosis, Gastroenterology, 78, 950, 10.1016/0016-5085(80)90776-3
Shmerling, 1970, Fecal fat and nitrogen in healthy children and in children with malabsorption and maldigestion, Pediatrics, 46, 690, 10.1542/peds.46.5.690
Milla, 1980, Small-intestinal absorption of amino acids and dipeptides in pancreatic insufficiency, 177
Shwachman, 1955, Mucoviscidosis, Adv. Pediatr., 7, 249, 10.1016/S0065-3101(22)00441-8
Gibbons, 1969, Disaccharides and cystic fibrosis of the pancreas, Arch. Dis. Child., 44, 63, 10.1136/adc.44.233.63
Durie, 1984, Pancreatic function testing in cystic fibrosis, J. Pediatr. Gastroenterol. Nutr., 3, 589
Durie, 1981, Plasma immunoreactive pancreatic cationic trypsinogen in cystic fibrosis: A sensitive indicator of exocrine pancreatic dysfunction, Pediatr. Res., 15, 1351, 10.1203/00006450-198110000-00010
Masoero, 1983, Serum trypsin-like immunoreactivity in cystic fibrosis, A.J.D.C., 137, 167
Chase, 1982, Linoleic acid absorption in children with cystic fibrosis, J. Pediatr. Gastroenterol. Nutr., 1, 49, 10.1097/00005176-198201010-00010
Hansen, 1983, Cystic fibrosis manifesting with acrodermatitis enteropathica-like eruption, Arch. Dermatol., 119, 51, 10.1001/archderm.1983.01650250055016
Kusoffsky, 1983, Prospective study of fatty acid supplementation over three years in patients with cystic fibrosis, J. Pediatr. Gastroenterol. Nutr., 2, 434, 10.1097/00005176-198302030-00007
Lloyd-Still, 1981, Essential fatty acid status in cystic fibrosis, and the effects of safflower oil supplementation, Am. J. Clin. Nutr., 34, 1, 10.1093/ajcn/34.1.1
Mischler, 1982, Correction of essential fatty acid deficiency in cystic fibrosis, Cystic Fibrosis Club Abstr., 23, 133
Deren, 1973, Malabsorption of crystalline vitamin B12 in cystic fibrosis, N. Engl. J. Med., 288, 949, 10.1056/NEJM197305032881808
Abernathy, 1976, Bulging fontanelle as presenting sign in cystic fibrosis: Vitamin A metabolism and effect on cerebrospinal fluid pressure, A.J.D.C., 130, 1360
Kulczycki, 1971, Malabsorption with vitamin A deficiency in a college girl treated for cystic fibrosis, Acta Pediatr. Scand., 60, 371
Scott, 1977, Rickets in adult cystic fibrosis with myopathy, pancreatic insufficiency, and proximal renal tubular dysfunction, J.A.M.A., 63, 451
Hahn, 1979, Reduced serum 25-hydroxy-vitamin D concentration and disordered mineral metabolism in patients with cystic fibrosis, J. Pediatr., 94, 38, 10.1016/S0022-3476(79)80346-7
Walters, 1972, Hemorrhagic diathesis and cystic fibrosis in infancy, A.J.D.C., 124, 641
Beckerman, 1979, Hypoelectrolytemia and metabolic alkalosis in infants with cystic fibrosis, Pediatrics, 63, 580, 10.1542/peds.63.4.580
Rapaport, 1981, The renin-angiotensin system in cystic fibrosis, J. Pediatr., 98, 768, 10.1016/S0022-3476(81)80841-4
Ruddy, 1982, Hypoelectrolytemia as presentation and complication of cystic fibrosis, Clin. Pediatr., 21, 367, 10.1177/000992288202100609
Orenstein, 1983, Exercise and heat stress in cystic fibrosis patients, Pediatr. Res., 17, 267, 10.1203/00006450-198304000-00007
Vichinsky, 1984, Inadequate erythroid response to hypoxia in cystic fibrosis, J. Pediatr., 105, 15, 10.1016/S0022-3476(84)80349-2
Halstead, 1970, Plasma zinc in health and disease, Lancet, 1, 322, 10.1016/S0140-6736(70)90701-4
Jacob, 1978, Zinc status and vitamin A transport in cystic fibrosis, Am. J. Clin. Nutr., 31, 638, 10.1093/ajcn/31.4.638
Roy, 1984, A rational approach to meeting macro- and micronutrient needs in cystic fibrosis, J. Pediatr. Gastroenterol. Nutr., 3, S154, 10.1097/00005176-198400031-00023
Harris, 1955, The effect of pancreatic therapy on fat absorption and nitrogen retention in children with fibrocystic disease of the pancreas, Arch. Dis. Child., 30, 424, 10.1136/adc.30.153.424
DiMagno, 1977, Fate of orally ingested enzymes in pancreatic insufficiency in man: Comparison of two dosage schedules, N. Engl. J. Med., 296, 1314, 10.1056/NEJM197706092962304
Mischler, 1982, Comparison of effectiveness of pancreatic enzyme preparations in cystic fibrosis, A.J.D.C., 136, 1060
Durie, 1980, Effect of cimetidine and sodium bicarbonate on pancreatic replacement therapy in cystic fibrosis, Gut, 21, 778, 10.1136/gut.21.9.778
Chase, 1979, Cystic fibrosis and malnutrition, J. Pediatr., 95, 337, 10.1016/S0022-3476(79)80504-1
Archibald, 1981, Assessment of the body composition and energy requirements of undernourished adolescents and young adults with cystic fibrosis, Cystic Fibrosis Club Abstr., 22, 93
Kraemer, 1978, Relative underweight in cystic fibrosis and its prognostic value, Acta Paediatr. Scand., 67, 3, 10.1111/j.1651-2227.1978.tb16273.x
Pencharz, 1983, Energy intakes and low-fat diets in children with cystic fibrosis, editorial, J. Pediatr. Gastroenterol. Nutr., 2, 400, 10.1097/00005176-198302030-00002
Bell, 1981, Nutrient intakes of adolescents with cystic fibrosis, J. Can. Diet. Assoc., 42, 62
Parsons, 1983, Energy needs and growth in children with cystic fibrosis, J. Pediatr. Gastroenterol. Nutr., 2, 44, 10.1097/00005176-198302010-00005
Berry, 1975, Dietary supplement and nutrition in children with cystic fibrosis, A.J.D.C., 129, 165
Yassa, 1978, Effects of an artificial diet on growth of patients with cystic fibrosis, Arch. Dis. Child., 53, 777, 10.1136/adc.53.10.777
Bertrand, 1984, Short-term clinical, nutritional, and functional effects of continuous elemental enteral alimentation in children with cystic fibrosis, J. Pediatr., 104, 41, 10.1016/S0022-3476(84)80586-7
Mansell, 1984, Short-term pulmonary effects of total parenteral nutrition in children with cystic fibrosis, J. Pediatr., 104, 700, 10.1016/S0022-3476(84)80947-6
Lippe, 1977, Pancreatic alpha and beta cell function in cystic fibrosis, J. Pediatr., 90, 751, 10.1016/S0022-3476(77)81241-9
Rosan, 1962, Diabetes mellitus and cystic fibrosis of the pancreas, A.J.D.C., 104, 625
Adrian, 1980, Hormonal abnormalities of the pancreas and gut in cystic fibrosis, Gastroenterology, 79, 460, 10.1016/0016-5085(80)90370-4
Matreshe, 1977, Meconium ileus equivalent complicating cystic fibrosis in postneonatal children and young adults, Gastroenterology, 72, 732, 10.1016/S0016-5085(77)80164-9
Rosenstein, 1983, Incidence of distal intestinal obstruction syndrome in cystic fibrosis, J. Pediatr. Gastroenterol. Nutr., 2, 299, 10.1097/00005176-198302020-00014
Dolan, 1975, Mild cystic fibrosis presenting as an asymptomatic distended appendiceal mass—a case report, Clin. Pediatr., 14, 862, 10.1177/000992287501400913
Mullins, 1965, Late intestinal complications of cysic fibrosis, J.A.M.A., 192, 741, 10.1001/jama.1965.03080220005001
Hodson, 1976, Meconium ileus equivalent in adults with cystic fibrosis of pancreas: A report of six cases, Br. Med. J., 2, 790, 10.1136/bmj.2.6039.790
Jaffe, 1966, Postinfancy intestinal obstruction in children with cystic fibrosis, Arch. Surg., 92, 337, 10.1001/archsurg.1966.01320210017003
Shwachman, 1975, Recurrent acute pancreatitis in patients with cystic fibrosis with normal enzymes, Pediatrics, 55, 86, 10.1542/peds.55.1.86
Stern, 1976, Symptomatic hepatic disease in cystic fibrosis: Incidence, course, and outcome of portal systemic shunting, Gastroenterology, 70, 645, 10.1016/S0016-5085(76)80247-8
Roy, 1982, Hepatobiliary disease in cystic fibrosis: A survey of current issues and concepts, J. Pediatr. Gastroenterol. Nutr., 1, 469, 10.1097/00005176-198212000-00005
Taylor, 1972, Neonatal jaundice associated with cystic fibrosis, A.J.D.C., 123, 161
Valman, 1971, Prolonged neonatal jaundice in cystic fibrosis, Arch. Dis. Child., 46, 809, 10.1136/adc.46.250.805
Craig, 1957, The pathological changes in the liver in cystic fibrosis of the pancreas, A.J.D.C., 93, 357
Oppenheimer, 1975, Hepatic changes in young infants with cystic fibrosis: Possible relation to focal biliary cirrhosis, J. Pediatr., 86, 683, 10.1016/S0022-3476(75)80351-9
Lloyd-Still, 1983, The liver in CF, 313
Dietzch, 1980, The value of bioptic follow-up examination for controlling the course of liver involvement in cytic fibrosis, 220
Gibson, 1977, Roentgenographically visible fatty liver in cystic fibrosis, Pediatrics, 59, 778, 10.1542/peds.59.5.778
Roy, 1980, Gastrointestinal and hepatobiliary complications: Changing pattern with age, 190
Esterly, 1962, Observations in cystic fibrosis of the pancreas: I. The gallbladder, Bull. Johns Hopkins Hosp., 110, 247
L'Heureux, 1977, Gallbladder disease in cystic fibrosis, A.J.R., 128, 953
Fernstersheib, 1979, Ultrasound evaluation of the hepatobiliary tract in cystic fibrosis, Pediatr. Res., 13, 398
Roy, 1977, Abnormal biliary lipid composition in cystic fibrosis: Effect of pancreatic enzymes, N. Engl. J. Med., 24, 1301, 10.1056/NEJM197712152972401
Schuster, 1977, The management of portal hypertension in cystic fibrosis, J. Pediatr. Surg., 12, 201, 10.1016/S0022-3468(77)80008-0
Holsclaw, 1971, Genital abnormalities in male patients with cystic fibrosis, J. Urol., 106, 568, 10.1016/S0022-5347(17)61343-0
Taussig, 1972, Fertility in males with cystic fibrosis, N. Engl. J. Med., 287, 586, 10.1056/NEJM197209212871204
Holsclaw, 1971, Increased incidence of inguinal hernia, hydrocele, and undescended testicle in males with cystic fibrosis, Pediatrics, 48, 442, 10.1542/peds.48.3.442
Rosen, 1971, Monotropic increase in serum FSH correlated with low sperm count in young men with oligospermia and aspermia, J. Clin. Endocrinol. Metab., 32, 410, 10.1210/jcem-32-3-410
Landon, 1984, Short stature and pubertal delay in male adolescents with cystic fibrosis, A.J.D.C., 138, 388
Matson, 1982, Pregnancy in the cystic fibrosis patient: An update, J. Reprod. Med., 27, 373
Moshang, 1980, Menarchal determinants in cystic fibrosis, A.J.D.C., 134, 1135
Oppenheimer, 1970, Observations on cystic fibrosis of the pancreas: VI. The uterine cervix, J. Pediatr., 77, 991, 10.1016/S0022-3476(70)80082-8
Cohen, 1980, Cystic fibrosis and pregnancy: A national survey, Lancet, 2, 842, 10.1016/S0140-6736(80)90183-X
Machida, 1981, Influence of progesterone on arterial blood and CSF and acid-base balance in women, J. Appl. Physiol., 51, 1433, 10.1152/jappl.1981.51.6.1433
Larsen, 1972, Cystic fibrosis and pregnancy, Obstet. Gynecol., 39, 880
Corkey, 1981, Pregnancy in cystic fibrosis: A better prognosis in patients with pancreatic function?, Am. J. Obstet. Gynecol., 140, 737, 10.1016/0002-9378(81)90732-8
Rosenstein, 1982, Cystic fibrosis: Diagnostic consideration, Johns Hopkins Med. J., 150, 113
Di Sant'Agnese, 1953, Sweat electrolyte disturbances associated with childhood pancreatic disease, Am. J. Med., 15, 777, 10.1016/0002-9343(53)90169-7
Gibson, 1959, A test for concentration of electrolyte in sweat in cystic fibrosis of the pancreas utilizing pilocarpine by iontophoresis, Pediatrics, 23, 545, 10.1542/peds.23.3.545
Stern, 1978, Intermediate-range sweat chloride concentration and Pseudomonas bronchitis: A cystic fibrosis variant with preservation of exocrine pancreatic function, J.A.M.A., 239, 2676, 10.1001/jama.1978.03280520048017
Andersen, 1960, Sweat tests results in normal persons of different ages compared with families with fibrocystic disease of the pancreas, Arch. Dis. Child., 35, 581, 10.1136/adc.35.184.581
Schoni, 1984, Early diagnosis of cystic fibrosis by sweat microspirometry, J. Pediatr., 104, 691, 10.1016/S0022-3476(84)80945-2
Denning, 1980, Cooperative study comparing three methods of performing sweat tests to diagnosis cystic fibrosis, Pediatrics, 66, 752, 10.1542/peds.66.5.752
Evans, 1981, Satisfactory screening for cystic fibrosis with the BM meconium procedure, J. Clin. Pathol., 34, 911, 10.1136/jcp.34.8.911
Hellsing, 1982, Meconium screening for cystic fibrosis, Acta Pediatr. Scand., 71, 827, 10.1111/j.1651-2227.1982.tb09527.x
Forrest, 1981, Screening for cystic fibrosis by a stool trypsin method, Arch. Dis. Child., 56, 151, 10.1136/adc.56.2.151
Dodge, 1982, Screening for cystic fibrosis: Current topics, Arch. Dis. Child., 57, 774, 10.1136/adc.57.10.774
Borgstrom, 1981, Immunoreactive trypsin, chymotrypsin, and pancreatic secretory trypsin inhibitor in cord blood from infants with cystic fibrosis, Acta Pediatrica. Scand., 70, 619, 10.1111/j.1651-2227.1981.tb05756.x
Wilcken, 1983, Cystic fibrosis screening by dried blood spot trypsin assay: Results in 75,000 newborn infants, J. Pediatr., 102, 383, 10.1016/S0022-3476(83)80653-2
Heeley, 1982, Screening for cystic fibrosis by dried blood spot trypsin assay, Arch. Dis. Child., 57, 18
Orenstein, 1977, The effect of early diagnosis and treatment in cystic fibrosis: A seven-year study, A.J.D.C., 131, 973
Wilcken, 1983, Diagnostic delay in cystic fibrosis: Lessons from newborn screening, Arch. Dis. Child., 58, 863, 10.1136/adc.58.11.863
Ad, 1983, Neonatal screening for cystic fibrosis: Position paper, Pediatrics, 72, 741, 10.1542/peds.72.5.741
Brock, 1984, Prenatal diagnosis of cystic fibrosis by amniotic fluid microvillar enzymes, Hum. Genet., 65, 248, 10.1007/BF00286511
Berlow, 1978, Enhanced dexamethasone resistance in cystic fibrosis cells: Potential use for heterozygote detection and prenatal diagnosis, Science, 201, 180, 10.1126/science.663650
Buttersworth, 1979, Primary amniotic fluid cells, skin fibroblasts and liver alpha fucosidase and its relation to cystic fibrosis, Clin. Chim. Acta, 92, 109, 10.1016/0009-8981(79)90103-7
Nadler, 1981, Prenatal detection of cystic fibrosis, Lancet, 2, 1226, 10.1016/S0140-6736(81)91458-6
Feigal, 1979, Altered intracellular calcium in fibroblasts from patients with cystic fibrosis and heterozygotes, Pediatr. Res., 13, 764, 10.1203/00006450-197906000-00009
Berlow, 1981, Distinguishing homozygote and heterozygote cystic fibrosis fibroblasts from normal cells by differences in sodium transport, N. Engl. J. Med., 304, 1, 10.1056/NEJM198101013040101
Lieberman, 1981, Presence of a serum hemagglutinin (lectin-like factor) in cystic fibrosis homozygotes and heterozygotes, J. Lab. Clin. Med., 97, 646
Wilson, 1979, Cystic fibrosis protein: A confirmed diagnostic marker for detecting heterozygote carriers: Significance in relation to future screening and to a proposed primary defect in alpha-2 macroglobulin, Pediatr. Res., 13, 1079, 10.1203/00006450-197909000-00028
Grataroli, 1984, Detection of the cystic fibrosis protein by iso-electric focusing of serum and plasma, Pediatr. Res., 18, 130, 10.1203/00006450-198402000-00003
Branchini, 1983, Identification of the major 4-methylumbelliferylguanidinobenzoate hydrolysing plasma protein in cystic fibrosis: Implication for intrauterine and heterozygote detection, Pediatr. Res., 17, 850, 10.1203/00006450-198311000-00003
Kurz, 1979, Killing of fibroblast by dexamethasone a dibutyl adesozine 3′ 5′ monophosphate is not a valid test for CF, Science, 206, 1317, 10.1126/science.229552
Seale, 1982, Current status of prenatal diagnosis and heterozygote detection of cystic fibrosis, Am. Clin. Lab. Sci., 12, 415
Gayton, 1977, Children with cystic fibrosis: Psychological test findings of patients, siblings, and parents, Pediatrics, 59, 888, 10.1542/peds.59.6.888
McCollum, 1970, Family adaptation to the child with cystic fibrosis, J. Pediatr., 77, 571, 10.1016/S0022-3476(70)80196-2
Venters, 1981, Familial coping with chronic and severe childhood illness: The case of cystic fibrosis, Soc. Sci. Med., 15A, 284
Kollberg, 1980, Cystic fibrosis in Sweden: A ten-year sociomedical follow-up, 256
McKeever, 1983, Siblings of chronically ill children: A literature review, with implications for research and practice, Am. J. Orthopsychiatr., 53, 209, 10.1111/j.1939-0025.1983.tb03366.x
Ellis, 1975, Growth, intelligence, and school performance in children with cystic fibrosis who have had an episode of malnutrition during infancy, J. Pediatr., 87, 565, 10.1016/S0022-3476(75)80822-5
Cowen, 1984, Growing older with cystic fibrosis: Psychologic adjustment of patients more than 16 years old, Psychosom. Med., 46, 363, 10.1097/00006842-198407000-00005
Levine, 1982, Sexual function in cystic fibrosis, Chest, 81, 422, 10.1378/chest.81.4.422
Corkey, 1983, Prognostic value of sweat chloride levels in cystic fibrosis: A negative report, Eur. J. Respir. Dis., 64, 434
Cropp, 1984, Heart-lung transplant in cystic fibrosis, Cystic Fibrosis Club Abstr., 25, 117